TALUSTA PECOMA, NADİR BİR OLGU VE LİTERATÜR DERLEMESİ

Year 2024, , 118 - 123, 03.06.2024

Turgut Kacan , Cahit Koçak , Berke Cenktuğ Korucu

https://doi.org/10.54270/atljm.2024.56

Abstract

Perivasküler epiteloid hücreli neoplazmlar (PEComalar), perivasküler epiteloid hücrelerden (PEC’ler) gelişen mezenkimal tümörlerdir. Yumuşak doku, iç
organlar ve deri en çok karşılaşılan vücut bölgeleridir. Primer kemik PEComaları, özellikle talusun PEComaları oldukça nadirdir; Bilgimize göre 2002’den bu
yana yalnızca 16 primer kemik PEComa vakası rapor edilmiştir. Biz de, talusta PEComa ile başvuran 51 yaşında bir erkek hasta ve literatür derlemesini rapor
ediyoruz.,

Keywords

PEComa, kemik PEComası, talus PEComası, ayak tümörü, yumuşak doku tümörü

Ethical Statement

Olgu sunumu olduğu için etik kurul onayı alınmamıştır

Supporting Institution

yok

Project Number

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Thanks

.

PECOMA OF THE TALUS, A RARE CASE AND THE LITERATURE REVIEW

Abstract

Perivascular epithelioid cell neoplasms (PEComas) are mesenchymal tumors which evolve out of the perivascular epithelioid cells (PECs).Soft tissue, visceral organs, and skin are the most encountered body regions. Primary bone PEComas,especially PEComas of talus, are remarkably rare; best of our knowledge, only sixteen primary bone PEComa cases have reported since defined in 2002. We report a 51-year-old male presented with PEComa of the talus and review the literature.

Keywords

PEComa, PEComa of bone, PEComa of talus, foot tumor, soft tissue tumor

Project Number

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