Wegener granulomatosis; multisystem involvement
Abstract
Wegener Granulomatozis (WG) is a systemic autoimmune disorder characterized by necrotizing granulomatous vasculitis that primarily affects the upper and lower respiratory tracts and kidneys. We report a case of WG with multisystem involvement. This 39-year-old man has ocular, paranasal, mediastinal, lung, splenic and meningeal involvement of WG. We describe and correlate the CT,US and cytological findings. W egener Granulomatosis (WG) is a disorder characterized by necrotizing granulomatous vasculitis that primarily affects the upper and lower respiratory tracts and kidneys (1,2). The classic form of WG is a multisystem process that includes respiratory tract granulomas, generalized vasculitis and glomerulonephritis, whereas the limited form of WG involves focal disease without glomerulonephritis (3). We report a case of WG with multisystem involvement.
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References
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