Elsberg Sendromu: Kauda Ekina Sendromunun Nedenlerinden Biri - Olgu Serisi ve Literatürün Gözden Geçirilmesi

Year 2023, Volume: 76 Issue: 4, 373 - 377, 05.04.2024

Aysun Genç

Abstract

Elsberg sendromu (ES), akut veya reaktif bir viral enfeksiyonu takiben omurilik alt bölgesinde sınırlı,akut veya subakut lumbosakral radikülit ve miyelit
ile karakterize nadir bir sendromdur. Bildirilen semptomlar idrar retansiyonu, bağırsak inkontinansı, radiküler ağrı ve kas güçsüzlüğüdür. Herpes
simpleks tip 2 enfeksiyonları veya dorsal kök gangliyonlarından reaktivasyon ile ilişkilidir, ayrıca akut batı Nil virüsü, varisella zoster virüsü ve Şiddetli
akut solunum yolu sendromu koronavirüs-2 ile bildirilen olgular da vardır. Klinisyenler genellikle bu sendromu akut kauda ekina sendromunun
ayırıcı tanısında değerlendirmez ve bu nedenle uygun tanısal yaklaşımlar gözden kaçar. Sarkoidoz, lenfoma, vaskülit, diğer enfeksiyon kaynakları ve
dural arteriyovenöz fistül de ayırıcı tanıda yer almaktadır. Post viral enflamatuvar bir durum olan ES’ye dikkat çekmek amacıyla akut kauda ekuina
sendromu bulguları gösteren ve ES tanısı alan iki olgu sunulacaktır.

Keywords

Elsberg Sendrom, Herpes Simpleks Virüs Tip 2, Miyelit

Project Number

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Elsberg Syndrome: One of the Causes of Cauda Equina Syndrome - A Case Series and Review of the Literature

Abstract

Elsberg syndrome (ES) is a rare syndrome characterized by acute or subacute lumbosacral radiculitis and myelitis confined to the lower spinal
cord, following an acute or reactivation viral infection. Reported complaints are urinary retention, bowel incontinence, radicular pain and muscle
weakness. It is associated with Herpes simplex type 2 infections or reactivation from dorsal root ganglia, there are also cases reported with acute
west Nile virus, varicella zoster virus and severe acute respiratory syndrome coronavirus 2. Clinicians do not generally consider this syndrome in
the differential diagnosis of acute cauda equina syndrome, and therefore, appropriate diagnostic approaches are missed. Sarcoidosis, lymphoma,
vasculitis, other sources of infection and dural arteriovenous fistula are also included in the differential diagnosis.
In order to draw attention to ES, which is a post viral inflammatory condition, two cases presenting acute cauda equina syndrome findings and
diagnosed with ES will be presented.

Keywords

Elsberg Syndrome, Herpes Simplex Type 2, Miyelitis

Ethical Statement

Informed consent taken from patients.

Supporting Institution

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Project Number

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Thanks

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References

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