Peutz Jeghers Sendromu

Year 1986, Volume: 39 Issue: 2, 207 - 213, 30.06.1986

Ali Özden

Abstract

Subileus ataklarıyla seyreden 13 yaşında Peutz Jeghers Sendromlu bir kadın hasta takdim edildi. İnce barsak ve kolon grafileri, gastro-intestinal endoskopi muayeneleri yapıldı. Mide, ince barsak ve kolonda polipler tesbit edildi. Barsak tıkanmasına yol açan büyük polip opere edildi ve hamartom polipi olarak tesbit edildi.
Bu sendrom ailevi olup ağız çevresi deri, dudak ve yanak mukozasında bazı vakalarda eller ve ayaklarda küçük melanin pigmenti toplanmasıyla kendini gösterir. İnce barsakta subileus nede -i niyle kolik tarzında karın ağrısı ve kusmaya yol açabilir. Tümör 3 cm'den büyük olabilir ve bizim vakamızda olduğu gibi tıkanma semptomlarına sebep olabilir.

Keywords

gastroenteroloji , makatta kan , vaka

Ethical Statement

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Supporting Institution

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Thanks

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Peutz-Jeghers Syndrome

Abstract

We report a case of Peutz-Jeghers Syndrome in a 13 years old female with subileus, Gastrointestinal x rays, gastrointestinal endos copic examination were done. She was found to have polyps in the stomach, small intestin, colon. Large polyp in the duodenume caused intestinal obstruction. She was operated. The polyp removed was hamartome. This syndrome is familial and usually recognized by the appearance of sınail melanotic spots on the perioral skin, lips, buccal mu-

Keywords

gastroentoloji , makatta kan , vaka

Ethical Statement

-

Supporting Institution

-

Thanks

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References

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