Az Bilinen Bir Konu ‘Rapunzel Sendromu’: Bir Olgu Sunumu

Öz

Trikobezoarlar, saç çekme (trikotillomani) ve saç yeme (trikofaji) alışkanlığı sonucu midede oluşan saç yumaklarıdır. Rapunzel sendromu gastrik trikobezoarın nadir bir formu olup, bezoarın kuyruk şeklinde uzantısının duodenuma geçmesi ile oluşmaktadır. Trikotillomaninin görülme sıklığı % 0.6-1.6 arasındadır. Hastaların %30’unda trikofaji gözlenir ve bunların sadece %1’inde cerrahi gerektirecek trikobezoarlar ortaya çıkar. Trikobezoarlara sıklıkla psikiyatrik bozukluklar eşlik eder ve genellikle kız ergenlerde görülür. Trikotillomani ve trikofajinin altında yatan neden tam olarak bilinmemekle birlikte, yatkınlık yaratan psikopatalojik nedenler  arasında stres, huzursuz aile ortamı, anne ve/veya baba kaybı, okul değişikliği gibi emosyonel etmenler sayılabilir. Tedavi genellikle psikiyatr ve dermatologların ortak katılımı ile olur. Bu çalışmada saç kaybı yakınması ile dermatolojiye başvurduktan sonra psikiyatri polikliniğine yönlendirilen 18 yaşındaki kadın olgu sunulmuştur.

Anahtar Kelimeler

• Rapunzel sendromu,trikobezoar,trikofaji

A Rare Known Topic 'Rapunzel Syndrome': A Case Report

Öz

Trichobezoars are concretions of hair casts in the stomach associated with trichotillomania and trichophagia. The Rapunzel syndrome is a rare form of gastric trichobezoar with a tail like extension into the intestine. The incidence of trichotillomania is between 0.6-1.6%. Trichophagia is observed in 30% of these patients, and only 1% of them have trichobezoars that require surgery. Trichobezoars are often accompanied by psychiatric disorders and are usually observed in adolescent girls. Although the underlying cause of trichotillomania and trichophagia, is not completely known, predisposing psychopathologic factors include emotional factors such as stress, restless family environment, loss of mother and /or father, and school change. The treatment of trichotillomania usually involves participation of both psychiatrists and dermatologists. In this study, we presented a case of 18 years old woman who was referred to the psychiatry outpatient clinic after admission of dermatology with complaint of hair loss.

Anahtar Kelimeler

• Rapunzel syndrome,trichobezoar,trichophagia

Kaynakça

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