Az Bilinen Bir Konu ‘Rapunzel Sendromu’: Bir Olgu Sunumu

Year 2018, Volume: 2 Issue: 2, 102 - 113, 09.07.2018

Beyza Mahmudoğlu Nursel Dilek Çiçek Hocaoğlu

Abstract

Trikobezoarlar, saç çekme (trikotillomani) ve saç
yeme (trikofaji) alışkanlığı sonucu midede oluşan saç yumaklarıdır. Rapunzel
sendromu gastrik trikobezoarın nadir bir formu olup, bezoarın kuyruk şeklinde
uzantısının duodenuma geçmesi ile oluşmaktadır. Trikotillomaninin görülme
sıklığı % 0.6-1.6 arasındadır. Hastaların %30’unda trikofaji gözlenir ve bunların
sadece %1’inde cerrahi gerektirecek trikobezoarlar ortaya çıkar.
Trikobezoarlara sıklıkla psikiyatrik bozukluklar eşlik eder ve genellikle kız
ergenlerde görülür. Trikotillomani ve trikofajinin altında yatan neden tam
olarak bilinmemekle birlikte, yatkınlık yaratan psikopatalojik nedenler  arasında stres, huzursuz aile ortamı, anne
ve/veya baba kaybı, okul değişikliği gibi emosyonel etmenler sayılabilir.
Tedavi genellikle psikiyatr ve dermatologların ortak katılımı ile olur. Bu
çalışmada saç kaybı yakınması ile dermatolojiye başvurduktan sonra psikiyatri
polikliniğine yönlendirilen 18 yaşındaki kadın olgu sunulmuştur.

Keywords

Rapunzel sendromu, trikobezoar, trikofaji

A Rare Known Topic 'Rapunzel Syndrome': A Case Report

Abstract

Trichobezoars
are concretions of hair casts in the stomach associated with trichotillomania
and trichophagia. The Rapunzel syndrome is a rare form of gastric trichobezoar with
a tail like extension into the intestine. The incidence of trichotillomania is
between 0.6-1.6%. Trichophagia is observed in 30% of these patients, and only
1% of them have trichobezoars that require surgery. Trichobezoars are often
accompanied by psychiatric disorders and are usually observed in adolescent
girls. Although the underlying cause of trichotillomania and trichophagia, is
not completely known, predisposing psychopathologic factors include emotional
factors such as stress, restless family environment, loss of mother and /or
father, and school change. The treatment of trichotillomania usually involves
participation of both psychiatrists and dermatologists. In this study, we
presented a case of 18 years old woman who was referred to the psychiatry
outpatient clinic after admission of dermatology with complaint of hair loss.

Keywords

Rapunzel syndrome, trichobezoar, trichophagia

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