İDİOPATİK HİPOPARATİROİDİZME BAĞLI 3 FAHR HASTALIĞI VAKASI Three Cases of Fahr Disease due to Idiopathic Hypoparathyroidism

Year 2016, Volume: 6 Issue: 2, 62 - 65, 19.12.2016

Elif Turan Sait Gönen Gülsüm Gönülalan Mustafa Kulaksızoglu Ahmet Kaya

Abstract

Bazal ganglionlarda bilateral kalsifikasyona bağlı nörolojik belirtiler Fahr hastalığı olarak bilinmektedir.

Fahr hastalığının etiyolojisinde; idiopatik, konjenital, kalsiyum bozuklukları; ağırlıklı olarak

hipoparatiroidiler, infeksiyonlar yer almaktadır. Bizim yazımızda hipoparatiroidiye bağlı bazal ganglionlarda

bilateral kalsifikasyon ve ekstrapiramidal semptomları olan üç vakadan bahsedilecek.

ABSTRACT

Bilateral calcifications in the basal ganglia associated with neurological manifestations have been

diagnosed as Fahr disease. The most frequent etiology of this syndrome is, together with idiopathic

causes and congenital, infections, calcium disorders, mainly primary hypoparathyroidism. We

present the cases of three patients with bilateral calcifications in the basal ganglia who presented

hypoparathyroidism and extra-pyramidal syndrome.

Keywords

Hipoparatiroidi

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