Yaygın anjiyosentrik düzenlenme ve kalsifikasyon gösteren pilositik astrositom: olgu sunumu

Year 2024, , 1107 - 1110, 30.12.2024

Ismail Saygin , Emel Çakır , Sevdegül Aydın Mungan , Uğur Yazar

https://doi.org/10.17826/cumj.1431427

Abstract

Pilositik astrositom (PA) çocukluk çağının en sık görülen glial tümörleridir. Genç yetişkinlerde de görülebilir. Tipik olarak serebellumda lokalizedir ve WHO grade 1 tümördür. Nadiren serebral hemisfer ve omurilikte de görülür. Kalsifikasyon PA için alışılmadık bir özelliktir. Anjiyosentrik dizilim veya psödorozet yapılar da PA'da görülen alışılmadık morfolojik paternlerdir ve literatürde az sayıda vaka bildirilmiştir. Prognoz genellikle iyidir. Supratentoryal PA'larda prognoz biraz daha kötü olma eğilimindedir. Burada diffüz anjiosentrik dizilim ve kalsifikasyon gösteren PA'lar ile “pilomiksoid astrositom, anjiosentrik gliom, papiller glionöronal tümör, astroblastom” gibi anjiosentrik dizilim veya perivasküler psödorosette gösteren tümörler arasındaki ayırıcı tanı tartışılmıştır.

Keywords

Pilositik astrositomlar, anjiyosentrik, psödorozet, kalsifikasyon

Ethical Statement

Etik beyana gerek yoktur.

Pilocytic astrocytoma with diffuse angiocentric arrangement and calcification: a case report

Abstract

Pilocytic astrocytoma (PA) is the most common glial tumors of childhood. It can also be seen in young adults. It is typically localized in the cerebellum and is a WHO grade 1 tumor. It is rarely seen in the cerebral hemisphere and spinal cord. Calcification is unusual feature for PA. Angiocentric arrangement or pseudorosette structures are also unusual morphologic patterns observed in PA, and few cases have been reported in the literature. Prognosis is usually good. The prognosis tends to be slightly worse in supratentorial PAs. In here the differential diagnosis between PAs with diffuse angiocentric arrangement and calcification and tumors with angiocentric arrangement or perivascular pseudorosette such as ‘‘pilomyxoid astrocytoma, angiocentric glioma, papillary glioneuronal tumor, astroblastoma” is discussed.

Keywords

Pilocytic astrocytomas, angiocentric, pseudorosette, calcification

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