Case Report

Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency

Volume: 42 Number: 3 September 30, 2017
Sedef Gülçin Ural , Meltem Aktay İnan
EN TR

Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency

Abstract

Glucose 6 phospate dehydrogenase (G6PD) deficiency is the most common enzyme deficiency. It is inherited in an X-linked recessive pattern and cause some disorders like hyperbilirubinemia in newborns, acut and chronic hemolysis. The first and main goal of the anethesia in this patient is to prevent oxidative stress. In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency

Keywords

Glucose 6 phospate dehydrogenase deficiency,anesthesia management,pediatric patient.

References

  1. 1. Reclos GJ, Hatzidakis CJ, Kruithof RA. G-6-PD Diagnosis: Modification of the standard method eliminates the need for an additional hemoglobin determination. Pharmakeftiki. 1999;12:25-31.
  2. 2. Glader BE. Glucose-6-phosphate dehydrogenase deficiency and related disorders of hexose monophosphate shunt and glutathione metabolism. In Wintrobe’s Clinical Hematology 10 th ed. (Eds GR Lee, J Foerster, J Lukens):1176-90. Baltimore, Williams & Wilkins, 2008.
  3. 3. Cheney CA, Lee A. Sequence of human G-6-PD cloned in plasmids and a yeast artificial chromosome (yac). Genomics. 1991;10:79-86.
  4. 4. Reclos GJ, Hatzidakis CJ, Schulpis KH. Glucose-6-phosphate dehyrogenase deficiency neonatal screening: preliminary evidence that a high percentage of partially deficient female neonates are missed during routine screening. J Med Screen. 2000;7:46-51.
  5. 5. Luzzatto L, Poggi V. Glucose 6 phosphate dehydrogenase deficiency and hemolytic anemia. In Nathan and Oski'sHematology of Infancy and Childhood, 7th ed. (Eds DG Nathan, SH Orkin):883-900. Philadelphia, Elsevier, 2009.
  6. 6. Salvati AM, Maffi D, Caprari P, Pasquino MT. G6PD deficiency and hereditary hemolytic anemia. Ann Ist Super Sanita. 1999;35:193-203.
  7. 7. Tamer I, Ünal B, Aksoy K. Glukoz-6-fosfat dehidrogenaz enzim eksikliği gözlenen olgularda eritrosit zarı Na+-K+/Mg++ 5’-trifosfataz, eritrosit süperoksit dismutaz ve plazma malondialdehit düzeyleri. Çukurova Üniversitesi Tıp Fakültesi Dergisi. 1998;23:114-8.
  8. 8. Beutler E. Screening for Glucose-6-Phosphate dehydrogenase deficiency. Israel J Med Sci. 1973;9:1350-2.
  9. 9. Valiaveedan S, Mahajan C, Rath GP, Bindra A, Manish MK. Anaesthetic management in patients with glucose-6-phosphate dehydrogenase deficiency undergoing neurosurgical procedures. Indian J Anaesth. 2011;55:68-70.
  10. 10. Elyassi AR, Rowshan HH. Perioperative management of the glucose-6- phosphate dehydrogenase deficient patient: a review of literature. Anesth Prog. 2009;56:86–91. 11. Chowdhry V, Bisoyi S, Mishra B. Perioperative challenges in a patient of severe G6PD deficiency undergoing open heart surgery. Ann Card Anaesth. 2012;15:50-3. 12. Altikat S, Ciftçi M, Büyükokuroğlu ME. In vitro effects of some anesthetic drugs on enzymatic activity of human red blood cell glucose 6-phosphate dehydrogenase. Pol J Pharmacol. 2002;54:67-71. 13. Büyükokuroğlu ME, Süleyman H. Glukoz 6-fosfat dehidrogenaz eksikliği. Turkiye Klinikleri Journal of Medical Sciences. 2001;21:415-9. 14. Younker D, DeVore M, Hartlage P. Malignant hyperthermia and glucose-6-phosphate dehydrogenase deficiency. Anesthesiology. 1984;60:601-3. 15. Smith CL, Snowdon SL. Anaesthesia and glucose-6-phosphate dehydrogenase deficiency: a case report and review of the literature. Anaesthesia. 1987;42:281-8. 16. Güneş Y, Özcengiz D, Özalevli M, Gündüz M, Işık G. Genel anestezi sırasında tanı konulan glukoz - 6 fosfat dehidrogenaz (G-6pd) Enzim Eksikliği. Çukurova Üniversitesi Tıp Fakültesi Dergisi. 2003;28:36-9.
APA
Ural, S. G., & İnan, M. A. (2017). Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Medical Journal, 42(3), 552-555. https://doi.org/10.17826/cutf.323982
AMA
1.Ural SG, İnan MA. Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Med J. 2017;42(3):552-555. doi:10.17826/cutf.323982
Chicago
Ural, Sedef Gülçin, and Meltem Aktay İnan. 2017. “Anesthesia Management in Pediatric Patient With Glucose 6 Phospate Dehydrogenase Deficiency”. Cukurova Medical Journal 42 (3): 552-55. https://doi.org/10.17826/cutf.323982.
EndNote
Ural SG, İnan MA (September 1, 2017) Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Medical Journal 42 3 552–555.
IEEE
[1]S. G. Ural and M. A. İnan, “Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency”, Cukurova Med J, vol. 42, no. 3, pp. 552–555, Sept. 2017, doi: 10.17826/cutf.323982.
ISNAD
Ural, Sedef Gülçin - İnan, Meltem Aktay. “Anesthesia Management in Pediatric Patient With Glucose 6 Phospate Dehydrogenase Deficiency”. Cukurova Medical Journal 42/3 (September 1, 2017): 552-555. https://doi.org/10.17826/cutf.323982.
JAMA
1.Ural SG, İnan MA. Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Med J. 2017;42:552–555.
MLA
Ural, Sedef Gülçin, and Meltem Aktay İnan. “Anesthesia Management in Pediatric Patient With Glucose 6 Phospate Dehydrogenase Deficiency”. Cukurova Medical Journal, vol. 42, no. 3, Sept. 2017, pp. 552-5, doi:10.17826/cutf.323982.
Vancouver
1.Sedef Gülçin Ural, Meltem Aktay İnan. Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency. Cukurova Med J. 2017 Sep. 1;42(3):552-5. doi:10.17826/cutf.323982