Organ Sparing Surgery for a Giant Liposarcoma

Year 2015, , 136 - 141, 09.10.2015

Hüseyin Aytaç Nurkan Törer Merve Özen İlker Arer

https://doi.org/10.17826/cutf.61520

Abstract

Liposarcomas those are malignant soft tissue tumors often occur in large sizes in the retroperitoneum and abdomen due to their silent clinic. Excision with negative margins is the gold standard of treatment. A case operated on for a giant intraabdominal liposarcoma is being reported. A giant soft tissue tumor filling the whole abdomen was determined in the computed tomography scan. Core biopsy was obtained and demonstrated a well-differentiated liposarcoma. A 15 kg of mass 44x30x14 cm in size was excised en-bloc. Pathological examination of this tumor showed a well-differentiated liposarcoma with mixoid parts. No recurrence was observed in two years of follow-up despite any adjuvant therapy. This is to be one of the largest retroperitoneal sarcomas in the literature

Keywords

Giant liposarcoma, retroperitoneal mass, intra-abdominal mass

Dev Liposarkom için Organ Koruyucu Cerrahi

Abstract

Malign yumuşak doku tümörleri olan liposarkomlar retroperitonda ve karın içinde sessiz klinikleri nedeniyle genellikle büyük boyutlarda karşımıza çıkmaktadır. Tedavide altın standart geride tümör bırakmadan yapılacak eksizyondur. Burada, ameliyat edilmiş karın içi dev bir liposarkom olgusu sunulmaktadır. Bilgisayarlı tomografide tüm karnı dolduran yer yer solid alanlar içeren bir yumuşak doku tümörü saptadı. Alınan tru-cut biyopsi bunun iyi diferansiye bir liposarkom olduğunu gösterdi. 15 kg ağırlığında ve 44x30x14 cm boyutundaki kitle tek parça halinde eksize edildi. Patolojik incelemede tümörün miksoid alanlar içeren iyi diferansiye bir liposarkom olduğu anlaşıldı. Ek tedavi olmaksızın iki yıllık sürede hastalık tekrarlaması gözlenmedi. Olgumuz literatürde sunulmuş en büyük retroperiton yerleşimli liposarkomlardan birisidir.

Keywords

Dev liposarkom, retroperitoneal kitle, intra-abdominal kitle

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