Anesthesia management in pediatric patient with glucose 6 phospate dehydrogenase deficiency

Year 2017, Volume: 42 Issue: 3, 552 - 555, 30.09.2017

Sedef Gülçin Ural Meltem Aktay İnan

https://doi.org/10.17826/cutf.323982

Abstract

Glucose 6 phospate dehydrogenase (G6PD) deficiency is the most common enzyme deficiency. It is inherited in an X-linked recessive pattern and cause some disorders like hyperbilirubinemia in newborns, acut and chronic hemolysis. The first and main goal of the anethesia in this patient is to prevent oxidative stress. In this case we aim to share applying general anesthesia safely in patients with G6PD deficiency

Keywords

Glucose 6 phospate dehydrogenase deficiency, anesthesia management, pediatric patient.

Glukoz 6 fosfat dehidrogenaz eksikliği olan pediatrik hastada anestezi yönetimi

Abstract

Glukoz 6 fosfat dehidrogenaz (G6PD) enzim eksikliği en sık görülen enzim eksikliğidir. X e bağlı resesif geçişli olan bu hastalık yenidoğan hiperbilirübinemisi, akut veya kronik hemoliz gibi bir dizi bozukluklara neden olur. Bu hastalar için genel anestezinin ilk ve temel hedefi oksidatif stres gelişimini önlemektir. Bu vakayı G6PD enzim eksikliği bulunan hastalarda genel anestezinin güvenli bir şekilde uygulanabileceğini vurgulamak amacı ile paylaşmayı amaçladık.

Keywords

Glukoz-6-fosfat dehidrogenaz eksikliği, anestezi yönetimi, çocuk hasta

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