Tekrarlayan Fasiyal Paralizili bir olgu: Melkersson-Rosenthal Sendromu

Derya Fatma Bulut; Gülen Gül Mert; Faruk İncecik; Özlem Mihriban Hergüner; Şakir Altunbaşak

doi:10.17826/cutf.72617

A Case with Recurrent Facial Palsy: Melkersson-Rosenthal Syndrome

Year 2014, Volume: 39 Issue: 4, 0 - , 22.07.2014

Derya Fatma Bulut Gülen Gül Mert Faruk İncecik Özlem Mihriban Hergüner Şakir Altunbaşak

https://doi.org/10.17826/cutf.72617

Abstract

Melkersson-Rosenthal syndrome (MRS) is a rare neuromucocutaneous syndrome characterized by recurrent facial paralysis, orofacial edema and fissured tongue. Oligosymptomatic and monosymptomatic forms are more common than the triad. The presence of two manifestations or one manifestation with granulomatous cheilitis in biopsy is sufficient to make diagnosis of Melkersson-Rosenthal syndrome. We present a 12 years-old male who is diagnosed Melkersson-Rosenthal syndrome.

Keywords

Melkersson-Rosenthal syndrome, recurrent facial paralysis, children.

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