Kartagener"s syndrome presented with nasal obstruction: A case report

Year 2014, Volume: 39 Issue: 4, 0 - , 22.07.2014

Suna Asilsoy Buket Kılıçaslan Cem Özer

https://doi.org/10.17826/cutf.48398

Abstract

The nasal polyposis is a chronic inflammatory process of the nasal mucosa. Although it is rare in children, there may be also association with cystic fibrosis and primary ciliary dyskinesia. About 50% of primary ciliary dyskinesia patients develop situs inversus and it is known as Kartagener"s syndrome. The Kartagener"s sydrome is a rare autosomal recessive disorder characterized by sinusitis, bronchiectasis, situs inversus. Clinically, patients present to the otolaryngologist with nasal obstruction. We as pediatricians, should consider nasal polyposis as a rare cause of nasal obstruction in children. In the presence of recurrent upper and lower respiratory tract infections accompanying nasal polyposis, Kartagener"s syndrome must be kept in mind as a rare reason.

Keywords

Nasal polyposis, Kartagener"s syndrome, primary ciliary dyskinesia, children

Burun tıkanıklığı ile gelen Kartagener sendromu: Bir olgu sunumu

Abstract

Nazal polipler, nazal mukozanın kronik enflamasyonundan kaynaklanan oluşumlardır. Çocuklarda nadir görülmekle birlikte saptandığında eşlik edebilecek kistik fibrozis ve primer silier diskinezi açısından dikkat edilmelidir. Primer silier diskinezili olguların %50"sinde situs inversus gösterilebilir; böyle olgular Kartagener sendromu olarak adlandırılır. Kartagener sendromu, otozomal resesif geçişli, sinüzit, bronşektazi ve situs inversus ile karakterize, nadir görülen bir durumdur. Klinik olarak en sık nazal tıkanıklık ile Kulak Burun Boğaz uzmanlarına başvururlar. Pediatristler olarak biz de, çocukluk çağında nazal tıkanıklığın nadir bir sebebi olarak nazal polipleri akla getirmeli; poliplere eşlik eden tekrarlayan üst ve alt solunum yolu enfeksiyonlarının varlığında ise nadir olarak görülen Kartagener sendromu akılda tutulmalıdır.

Keywords

Nazal polipozis, Kartagener sendromu, primer silier diskinezi, çocuklar

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• Yazışma Adresi / Address for Correspondence: Dr. Buket Kılıçaslan Başkent Üniversitesi Adana Uygulama ve Araştırma Merkezi Çocuk Sağlığı ve Hastalıkları Anabilim Dalı ADANA E-mail: [e-mail] G eliş tarihi/Received on : 13.05.2014
• Kabul tarihi/Accepted on: 06.06.2014