A Rare Case: Sporadic Bladder Paraganglioma

Year 2013, Volume: 38 Issue: 4, 794 - 799, 01.12.2013

Hakan Erçil Umut Ünal Güçlü Gürlen Nevzat Can Şener Tardu Çınar Yalçın Evliyaoğlu

Abstract

Paraganglioma is a rare tumor which originates from paraganglia tissue from neural crest. Bladder paraganglioma is suggested to be from crommaffin cells by the remains of the embryological cells. In this report, we aimed to discuss the literature by a case of bladder paraganglioma. A 39 year old male applied to our clinic with gross hematuria. A 2x2 cm mass was revealed in urinary ultrasound. Paraganglioma was found in the resection specimen and partial cystectomy was performed to the patient. A six month follow up revealed no recurrences. Even though bladder paraganglioma is a rare disease, it should be kept in mind for differential diagnosis.

Keywords

partial cystectomy, bladder, paraganglioma

Nadir Bir Olgu: Sporadik Mesane Paraganglioması

Abstract

Paraganglioma nadir olarak görülen ve nöral krest orjinli paraganglia dokusundan gelişen bir tümördür. Mesane paraganglioması, mesane duvarı içinde kromaffin hücrelerin embriyojenik artıklarından kaynaklandığı öne sürülmüştür. Biz bu çalışmamızda mesanede yerleşen primer paraganglioma olgusunu literatür eşliğinde irdeledik. 39 yaşında erkek hasta iki yıldır ağrısız pıhtılı idrar yapma şikayetiyle başvurduğu polikliniğimizde yapılan idrar tahlilinde hematürisi olması üzerine yapılan ultrasonografisinde mesanede 2x2 cmlik kitle saptandı. Patolojisi paraganglioma gelen hastaya parsiyel sistektomi uygulandı. Hastanın 6 aylık takiplerine nüks izlenmedi. Mesane paragangliomasi nadir bir olgu olsa da, mesane tümörü ayırıcı tanısında mutlaka akla getirilmelidir.

Keywords

Parsiyel Sistektomi, Mesane, Paraganglioma

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