Gluteal Congenital Fibrous Hamartoma of Infancy: A Case Report

Year 2013, Volume: 38 Issue: 2, 333 - 337, 01.06.2013

Begül Yağcı-küpeli Arbay Ozden Ciftci Bilgehan Yalçın Mithat Haliloglu Zuhal Akçören Münevver Büyükpamukçu

Abstract

Fibrous hamartoma of infancy (FHI) is a rare benign subcutaneous tumor which is commonly seen in the first year of life. Patients usually present with a single, painless, rapidly growing mass located mostly on the upper extremities. It can be difficult to distinguish this lesion from the malignant soft tissue sarcomas because of the rapid growth and radiological characteristics. Here we report a 5-month-old boy with a large gluteal mass and cutaneous findings which was initially thought to be an infiltrative malignant tumor and finally diagnosed as FHI.

Keywords

Fibrous hamartoma of infancy, congenital, gluteal

Konjenital Infantil Fibröz Hamartom: Bir Olgu Sunumu

Abstract

İnfantil fibröz hamartom sıklıkla hayatın ilk yılında görülen, nadir ve benign bir subkutan tümördür. Hastalar genellikle üst ekstremite yerleşimli ağrısız ve hızlı büyüyen bir kitle nedeniyle başvurmaktadır. Kitlenin radyolojik özellikleri ve hızlı büyüme özelliği nedeniyle yumuşak doku sarkomlarından ayırt edilmesi zor olabilir. Burada büyük bir gluteal kitle ile başvuran 5 aylık bir erkek çocukta infiltratif malign tümör özellikleri gösteren fibröz hamartom olgusu sunulmaktadır.

Keywords

İnfantil fibröz hamartom, konjenital, gluteal

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