Anesthesia management in a patient with Dandy-Walker Syndrome and Fontan physiology

Year 2021, Volume: 46 Issue: 3, 1318 - 1320, 30.09.2021

Nilgün Alpay , Sibel Tetiker

Abstract

Dental treatment in patients with syndromes is often difficult and general anesthesia is needed most of the time. Dandy-Walker Syndrome with Fontan physiology patients is one of these patient groups that need extra attention. Especially due to abnormal facial (cleft lip and/or palate) and head features (hydrocephalus) of these patients result in intracranial pressure increases, epilepsy and an increase of difficult intubation,possibility. In addition, extra physiological disturbances brought by the Fontan physiology and cardiovascular anomaly may cause sudden decreases in saturation or vital arrhythmias. However, with an accurate and complete preparation, general anesthesia can be safely performed in this patient group as well.

Keywords

General anesthesia, Dandy- Walker Syndrome, Fontan physiology

Dandy-Walker Sendromu ve Fontan fizyolojili bir hastada anestezi yönetimi

Abstract

Sendromlu hastalarda dentalı tedavi genellikle zordur ve genel anesteziye ihtiyaç duyulur. Fontan fizyolojili, Dandy Walker Sendromuna sahip hastalar da özel dikkat isteyen hasta gruplarından biridir. Bu hastalarda anormal fasiyal (Yarık damak-dudak) ve kafa (hidrosefalik) yapılarından dolayı intrakranial basınç artışı, epilepsi ve zor entübasyon olasılığı yüksektir. yrıca fFontan fizyolojinin ve kardiyovasküler anamalinin getirdiği ekstra fizyolojik bozukluklar ani saturasyon düşmesi ya da hayati aritmiler olabilir. Ayrıca Fontan fizyolojinin ve kardiyovasküler anomalinin getirdiği ekstra fizyolojik bozukluklar ani saturasyon düşmesi ya da hayati aritmilere neden olabilir.Buna rağmen doğru ve kapsamlı bir hazırlıkla genel anestezinin bu hasta grubunda da kullanılması mümkündür.

Keywords

Dandy- Walker syndrome,, Fontan physiology, General anesthesia

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