ANESTHESIA MANAGEMENT IN PATIENT WITH FAHR’S SYNDROME: A CASE REPORT

Year 2018, , 141 - 143, 27.08.2018

Engin Kıvrak

https://doi.org/10.5505/deutfd.2018.25633

Abstract

Fahr’s syndrome is a
neurodegenerative disease characterized by symmetric intracranial
calcifications in areas such as the cerebellum and basal ganglia. Detection and
treatment of hypocalcemia in this disorder, where calcium and phosphorus
metabolism is impaired, is important for anesthesia application. This article
describes the general anesthesia management of a 64-year-old patient with Fahr’s
syndrome associated with hypoparathyroidism.

Keywords

Fahr’s syndrome, basal ganglis diseases, anesthesia, hypocalcemia, hypoparathyroidism

Fahr Sendromu Olan Hastada Anestezi Yönetimi: Olgu Sunumu

Abstract

Fahr sendromu, serebellum, bazal
gangliyonlar gibi alanlarda simetrik intrakraniyal kalsifikasyonlarla
karakterize nörodejeneratif bir hastalıktır. Kalsiyum ve fosfor
metabolizmasının bozuk olduğu bu hastalıkta hipokalseminin tespit ve tedavisi
anestezi uygulaması açısından önem taşımaktadır. Olgu sunumunda 64 yaşında
hipoparatiroidi ile ilişkili Fahr Sendromu tanısı olan hastanın genel anestezi
yönetimi irdelenmiştir.

Keywords

Fahr Sendromu, bazal ganglia hastalıkları anestezi, hipokalsemi, hipoparatiroidizm

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