Öz
Fahr’s syndrome is a
neurodegenerative disease characterized by symmetric intracranial
calcifications in areas such as the cerebellum and basal ganglia. Detection and
treatment of hypocalcemia in this disorder, where calcium and phosphorus
metabolism is impaired, is important for anesthesia application. This article
describes the general anesthesia management of a 64-year-old patient with Fahr’s
syndrome associated with hypoparathyroidism.
Anahtar Kelimeler
Fahr’s syndrome basal ganglis diseases anesthesia hypocalcemia hypoparathyroidism
Kaynakça
- Saleem S, Aslam HM, Anwar M, et al. Fahr’s syndrome: literature review of current evidence. Orphanet J Rare Dis. 2013;8:156. doi:10.1186/1750-1172-8-156.
- Swami A, Kar G. Intracranial hemorrhage revealing pseudohypoparathyroidism as a cause of fahr syndrome. Case Rep Neurol Med. 2011;2011:407567. doi:10.1155/2011/407567.
- Ramisa J, Ibanez AE, Irigoína RR, Artigasa CF, Comasa LM. Extrapyramidal symptoms due to calcinosiscerebri in a patient with unknown primary hypoparathyroidism. Endocrinol Nutr. 2012;59:69-71.
- El Boukhrissi F, Zoulati G, En-nafaa I, et al. Fahr syndrome secondary to primary hypoparathyroidism: about a case. Pan Afr Med J. 2017;26:2. doi:10.11604/pamj.2017.26.2.10689.
- Marinković, DM, Dragović, T, Kiković, S, Kuzmić-Janković, S, Djuran, Z, Hajduković, Z. Fahr's syndrome and idiopathic hypoparathyroidism: A case report. Vojnosanit Pregl. 2017;74(2), 184-188.
- Soares, F, Amorim, F, Santana, A, Moura, E, Margalho, S, Amorim, A, Maia, M, Vasconcelos, F. Fahr’s Syndrome due to Hypoparathyroidism Following Thyroidectomy. J Med Cases. 2013;4: 380-384.
- Baum VC, O’Flaherty JE. Anesthesia for Genetic, Metabolic, and Dysmorphic Syndromes of Childhood. 2nd edition, Philadelphia: Lippincott Williams & Wilkins; 2007. p. 129.
- Okçelik S, Tasdemir S, Öztürk E, Soydan H. Subinguinal Varicocelectomy under Spinal Anesthesia in a Fahr’s Syndrome Patient with Non-Obstructıve Azoospermia. Andrology (Los Angel). 2016; 5:163. doi:10.4172/2167-0250.1000163.
- Aguilera IM, Vaughan RS. Calcium and the anaesthesist. Anaesthesia. 2000;55:779–90.
- Belenli C, Arpaci AH. Anesthesiological approach to a case with FAHR syndrome. J Res Med Sci. 2014;19:286.
Öz
Fahr sendromu, serebellum, bazal
gangliyonlar gibi alanlarda simetrik intrakraniyal kalsifikasyonlarla
karakterize nörodejeneratif bir hastalıktır. Kalsiyum ve fosfor
metabolizmasının bozuk olduğu bu hastalıkta hipokalseminin tespit ve tedavisi
anestezi uygulaması açısından önem taşımaktadır. Olgu sunumunda 64 yaşında
hipoparatiroidi ile ilişkili Fahr Sendromu tanısı olan hastanın genel anestezi
yönetimi irdelenmiştir.
Anahtar Kelimeler
Fahr Sendromu bazal ganglia hastalıkları anestezi hipokalsemi hipoparatiroidizm
Kaynakça
- Saleem S, Aslam HM, Anwar M, et al. Fahr’s syndrome: literature review of current evidence. Orphanet J Rare Dis. 2013;8:156. doi:10.1186/1750-1172-8-156.
- Swami A, Kar G. Intracranial hemorrhage revealing pseudohypoparathyroidism as a cause of fahr syndrome. Case Rep Neurol Med. 2011;2011:407567. doi:10.1155/2011/407567.
- Ramisa J, Ibanez AE, Irigoína RR, Artigasa CF, Comasa LM. Extrapyramidal symptoms due to calcinosiscerebri in a patient with unknown primary hypoparathyroidism. Endocrinol Nutr. 2012;59:69-71.
- El Boukhrissi F, Zoulati G, En-nafaa I, et al. Fahr syndrome secondary to primary hypoparathyroidism: about a case. Pan Afr Med J. 2017;26:2. doi:10.11604/pamj.2017.26.2.10689.
- Marinković, DM, Dragović, T, Kiković, S, Kuzmić-Janković, S, Djuran, Z, Hajduković, Z. Fahr's syndrome and idiopathic hypoparathyroidism: A case report. Vojnosanit Pregl. 2017;74(2), 184-188.
- Soares, F, Amorim, F, Santana, A, Moura, E, Margalho, S, Amorim, A, Maia, M, Vasconcelos, F. Fahr’s Syndrome due to Hypoparathyroidism Following Thyroidectomy. J Med Cases. 2013;4: 380-384.
- Baum VC, O’Flaherty JE. Anesthesia for Genetic, Metabolic, and Dysmorphic Syndromes of Childhood. 2nd edition, Philadelphia: Lippincott Williams & Wilkins; 2007. p. 129.
- Okçelik S, Tasdemir S, Öztürk E, Soydan H. Subinguinal Varicocelectomy under Spinal Anesthesia in a Fahr’s Syndrome Patient with Non-Obstructıve Azoospermia. Andrology (Los Angel). 2016; 5:163. doi:10.4172/2167-0250.1000163.
- Aguilera IM, Vaughan RS. Calcium and the anaesthesist. Anaesthesia. 2000;55:779–90.
- Belenli C, Arpaci AH. Anesthesiological approach to a case with FAHR syndrome. J Res Med Sci. 2014;19:286.
Ayrıntılar
| Birincil Dil | Türkçe |
|---|---|
| Konular | Sağlık Kurumları Yönetimi |
| Bölüm | Makaleler |
| Yazarlar | |
| Yayımlanma Tarihi | 27 Ağustos 2018 |
| Gönderilme Tarihi | 20 Temmuz 2017 |
| Yayımlandığı Sayı | Yıl 2018 |