Neurourological complications in patients with myelodisplasia

Abstract

Spina bifida yaşamla bağdaşan konjenital anomaliler arasında sık rastlanılan patolojilerdendir. Embriyolojik dönemde nöral tüpün kapanma defektleri açık ya da kapalı spinal disrafizmle sonuçlanır. Günümüzde nöroşirurjikal tekniklerin ilerlemesiyle hastaların multidisipliner takibi, yaşam kaliteleri açısından önem kazanmıştır. Ürolojik komplikasyonların önlenmesi ve tespit edilmesi bakımından da bazı yaklaşımlar standardize edilmiştir. Olguların uzun dönem takibinde nöroşirurjikal açıdan prognozun yanı sıra eşlik edebilen tüm patolojilerin akılda tutulması ve bu amaçla hastaya yön gösterilmesi önemlidir. Bu yazıdaki amaç Spina bifida hastalarında mevcut olabilecek ürolojik problemleri ve bunlarla ilgili son çalışmaları gözden geçirmektir.

Keywords

• Spina bifida, spinal disrafizm, üriner inkontinans, nörojenik mesane

Neurourological complications in patients with myelodisplasia

Abstract

Spina bifida is a frequently seen congenital anomaly which is compatible with life. During the embryological period the defects in the closure of neural tube leads to open or closed spinal dysraphism. At the present day with the improving neurochirurgical techniques, the patients multidisciplinary follow-ups became important as a matter of the health quality. To prevent and to determine the urological complications some approaches became standardized. In the long term period all accompanying pathologies have to be beared in the mind in addition to neurosurgical prognosis and the patients must have to be guided indeed. The aim of this review is to look over the urological problems and the last studies about these problems in spina bifida patients.

Keywords

• Spina bifida, spinal dysraphism, urinary incontinence, neurogenic bladder

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