Aksiller lokalizasyonu olan nadir yüksek dereceli miksofibrosarkom olgusu

Yıl 2020, , 35 - 38, 21.04.2020

Yeliz Yılmaz Bozok , Murat Kemal Atahan , Furkan Tosun , Sultan Deniz Altındağ , Asli Kahraman Akkalp

https://doi.org/10.33713/egetbd.655419

Öz

Miksofibrosarkom nadir görülen yumuşak bir doku sarkomudur. Çoğunlukla ekstremitelerde lokalizedir. Kesin tanı histopatolojik inceleme ile yapılsa da, görüntüleme yöntemleri derecelendirme ve tedavi planlamasında önemli rol oynamaktadır. Aksiller bölge nadiren dahil olabilse de literatürde bildirilmiş bir durum yoktur. Tümörün bol miktarda nörovasküler bir yapıya sahip olması göz önüne alındığında, tümörün geniş cerrahi marjlarla eksize edilmesi zordur. Olgumuz literatürde aksiller lokalizasyonu olan ilk olgu olduğu için dikkat çekicidir. Geniş marjlı cerrahi eksizyon tedavinin en önemli basamağıdır. R0 rezeksiyonu sağkalım üzerinde önemli bir etkiye sahiptir. Sonuç olarak, aksiller MFS'de kemoterapinin ardından geniş cerrahi eksizyonun lokal nüksü azaltmada olumlu bir katkısı olacağını düşünüyoruz

Anahtar Kelimeler

Miksofibrosarkom, Aksilla, Malign, Nadir

A case of high-grade myxofibrosarcoma with rare axillary localization

Öz

Myxofibrosarcoma is a rare soft tissue sarcoma. It is mostly localized at extremities. Although definitive diagnosis is made by histopathological examination, imaging modalities play an important role in grading and treatment planning. Although axillary region can be involved rarely, there is no reported case in the literature. Given that tumor has an abundant neurovascular structure, it is challenging to excise tumor with wide surgical margins. Our case is striking as it is the first case with axillary localization in the literature. The surgical excision with wide margin is the most important step of the treatment. The R0 resection has an important impact on survival. In conclusion, we think that, in axillary MFS, wide surgical excision followed by chemotherapy will have positive contribution in reducing local recurrence.

Anahtar Kelimeler

Myxofibrosarcoma, Axilla, Malign, Rare

Kaynakça

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