Primary Splenic angiosarcoma a case report and literature review

Yıl 2019, Cilt: 2 Sayı: 1, 31 - 33, 01.04.2019

Murat Güner , Nurullah Damburacı , Mehmet Gündoğan Utku Dönem Dilli Coşkun Ege Oğuzer Barış Sevinç

https://doi.org/10.33713/egetbd.476284

Öz

Primary
splenic angiosarcoma is a very aggressive neoplasm with poor prognosis due to
its very high frequency of metastasis. The tumor cells exhibit a strong positivity for at least one of the
endothelial markers (CD31, CD34, and factor VIII).
The diagnosis is usually difficult and late because the patient remains
asymptomatic till the onset of massive intra-abdominal bleeding. Early diagnosis and surgical management is the only
potentially long –term therapeutic option. The current and accepted therapy is
splenectomy.  Herein, we
report a case of primary splenic angiosarcoma that presented with abdominal
pain, along with a review of the current literature.

Anahtar Kelimeler

spleen, anjiosarcoma, splenectomy

Primer dalak anjisorkom olgu sunumu ve literatür eşliğinde değerlendirme

Öz

Primer dalak anjiosarkom nadir görülen ,
sık metastaz yapabilen ,kötü prognozlu, agresif bir neoplazidir. Tümör
hücreleri endotelyal markerlar (CD31, CD34, and faktör VIII) ile güçlü pozitiflik göstermektedir.Erken dönemde
asemptomatik olduğu için hastalar ancak rastlantısal olarak veya karın içi
kanama bulguları gibi nedenlerle geç dönemde tanı alabilmektedir.Erken tanı ve
cerrahi girişim en etkili tedavi yöntemidir.Kabul edilen tedavi yöntemi
splenektomidir.Bu çalışmada kliniğimize karın ağrısı ile başvuran ve primer
dalak anjiosarkom tanısı alan hasta literatür eşliğinde değerlendirilmiştir.

Anahtar Kelimeler

dalak, anjiosarkom, splenektomi

Kaynakça

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