A Giant Hamartoma of Tuber Cinerium: Conventional MRI Imaging and MR Spectroscopy Findings

Abstract

Hypothalamic hamartoma is a developmental malformation in the region of tuber cinereum and mamillary bodies. It presents the most commonly detectable lesion in patients with precocious puberty and is associated with gelastic seizures. As well as, it can be completely silent to be found only incidentally. Computed tomography (CT) and magnetic rezonans (MR) imaging are preferred imaging modalities in diagnose of hypothalamic hamartomas. The aim of this study is to present the radiologic imaging findings of a rare hypothalamic hamartoma case.

Keywords

• Hypothalamic hamartoma, giant, tuber cinerium, MR imaging, spectroscopy

A Giant Hamartoma of Tuber Cinerium: Conventional MRI Imaging and MR Spectroscopy Findings

Öz

Hipotalamik hamartoma tuber sineryum bölgesinde ve mamilalar cisimciğinin bir gelişimsel anomalisidir. Bu yaygın olarak puberte öncesi dönemde saptanabilmekte ve gelastic nöbetler ile ilişkilidir. Tamamen sessiz olabilir. ve tesadüfen tespit edilebilir. Bilgisayarlı tomografi (BT) ve manyetik rezonans (MR) görüntüleme hipotalamik hamartomların tanısında görüntüleme yöntemleri olarak tercih edilmektedir. Bu çalışmanın amacı nadir bir hipotalamik hamartomu olgusunun radyolojik görüntüleme bulgularını sunmaktır

Anahtar Kelimeler

• Hipotalamik hamartom, dev, tuber sineryum, MR bulguları, spektroskopi

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