Primary Hiperplastic Persistant Vitreus: A Case Report

Abstract

Persistent hyperplastic primary vitreous (PHPV) is a disorder of ocular development which occurs due to incomplete regression of the embryonic vitreous and hyaloid vasculature. Most cases of PHPV are sporadic and unilateral. We report a case of PHPV in a 5-year-old male who presented with complaint of decreasing eye size. Grey-scale ultrasonography (US) evaluation revealed an hypoechogenic band in the posterior segment of the left globe extending from the posterior surface of the lens capsule to the optic disc. Also magnetic resonance imaging (MRI) findings suggested the diagnosis of persistent hyperplastic primary vitreous.

Keywords

• Persistent hyperplastic primary vitreous, imaging, MRI, ultrasound

Primary Hiperplastic Persistant Vitreus: A Case Report

Öz

Persistan hiperplastik primer vitreus (PHPV) embriyonik vitreusun inkomplet regresyonuna bağlı olarak ortaya çıkan gelişimsel oküler bir hastalıktır. PHPV vakalarının birçoğu sporadiktir ve tek taraflı görülür. Bu yazıda gözde küçülme şikayeti ile başvuran 5 yaşındaki PHPV olgusu sunuldu. Ultrasonografi (USG) incelemesinde sol glob posterior segmentinde, lens posteriorundan optik diske uzanan hipoekoik bant görüldü. Aynı zamanda magnetik rezonans görüntüleme (MRG) bulguları da PHPV tanısını destekledi

Anahtar Kelimeler

• Persistan hiperplastik primer vitreus, görüntüleme, MRG, ultrasonografi

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