Imaging Features of Isolated Unilateral Pulmonary Artery Agenesis: a review of four cases

Year 2013, Volume: 10 Issue: 12, - , 21.03.2016

Abdussamet Batur Kemal Ödev Sevgi Pekcan

Abstract

To highlight the variation in imaging and clinical manifestations of four cases of isolated unilateral absence of pulmonary artery presented in varied ages. Four patients with unilateral pulmonary artery agenesis were referred to our institution They underwent a series of investigations, including chest radiography, computed tomography and magnetic resonance imaging. Two of the four patients had absence of the right main pulmonary artery, while the remaining two patients had absence of the left main pulmonary artery. All patients showed a restrictive defect on pulmonary function tests. Radiography, CT and MRI confirmed the anatomy and the presence of multiple collaterals. Isolated unilateral pulmonary artery agenesis has a non-specific presentation. Awareness of this condition can lead to earlier diagnosis, with cross-sectional imaging making an important contribution.

Keywords

Pulmonary artery agenesis, radiologic findings, clinical features

Imaging Features of Isolated Unilateral Pulmonary Artery Agenesis: a review of four cases

Abstract

Farklı yaş ve farklı klinik bulgularla başvuran izole tek taraflı pulmoner arter agenezili dört olgunun radyolojik bulgularını sunmak. İzole taraflı pulmoner arter agenezis tanılı dört hastanın klinik bilgileri ile birlikte direkt grafi, bilgisayarlı tomografi (BT) ve manyetik rezonans görüntüleme (MRG) bulguları değerlendirildi. İki olguda sağ pulmoner arter yokluğu, diğer iki olguda ise sol pulmoner arter yokluğu izlendi. Tüm hastaların solunum fonksiyon testlerinin hafif düzeyde restriktif paternle uyumlu olduğu görüldü. Direkt grafi, BT ve MRG tetkiklerinde akciğerlerin anatomik yapısı ve gelişen kollateral yapılar görüntülendi. İzole tek taraflı pulmoner arter agenezisi olan olgular spesifik olmayan semptomlarla başvururlar. Dikkatli bir yaklaşımla bu hastalarda erken tanıya gidilebilir. Görüntüleme yöntemleri oldukça yararlı bilgiler sağlamaktadır

Keywords

Pulmoner arter agenezisi, radyolojik bulgular, kilinik özellikler

References

• Okutan O, Ugan H, Kaya H, et al. Isolated Unilateral Pulmonary Artery Agenesis. Turkish Cardiovasc Thorax Surg J 2010;18(1): 67-70.
• Bouros D, Pare P, Panagou P, Tsintiris K, Siafakas N. The varied manifestation of pulmonary artery agenesis in adulthood. Chest 1995; 108: 670-6.
• Ten Harkel AD, Blom NA, Ottenkamp J. Isolated unilateral absence of a pulmonary artery: A case report and review of the literature. Chest 2002; 122: 1471-7.
• Mello Junior WT, Nogueira JRC, Santos M, França WJP. Isolated absence of the right pulmonary artery as a cause of massive hemoptysis. Interact Cardiovasc Thoracic Surg 2008; 7: 1183-5.
• Bilgiç İ, Uçan ES. Krall WR, Ploy-Song-Sang Y. Unilateral pulmonary artery aplasia presenting with chest pain and pleural effusion. South Med J 1980; 73: 233–6.
• Lin YM, Liang KW, Ting CT. Unilateral pulmonary artery- agenesis with presentation of hemoptysis: a case report. Chung Hua I Hsueh Tsa Chih (Taipei) 1999; 62:644–7