Von Willebrand Disease type 2B: A diagnostic dilemma

Abstract

A young female presented with isolated chronic unilateral intractable epistaxis with non healing granular mass in the left nasal cavity.  Histopathological examination was reported as acute and chronic non specific inflammation which did not respond to antibiotics or steroid.  After ten years follow up she was finally diagnosed to have Von Willebrand disease type 2B. This is the first case report of von Willebrand disease presenting with intermittent epistaxis as its sole disease manifestation. Although epistaxis is a common complaint in Otorhinolaryngology clinics, this case posed a diagnostic dilemma.

Keywords

• Type 2 von Willebrand Disease
• epistaxis
• isolated
• Wegener’s Granulomatosis

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