Subcutaneous dermatofibrosarcoma protuberans in parotid region: Case report

Year 2013, Volume: 18 Issue: 4, 198 - 201, 14.03.2014

Mehmet Garça Mustafa Kösem Mahfuz Turan Nazım Bozan Hakan Çankaya

Abstract

Dermatofibrosarcoma protuberans (DFSP) is a low-grade soft tissue sarcoma (fibrosarcoma) originated from dermal and subdermal layer of the skin. But subcutaneous localization is quite rare. It is one of the rare tumors and accounts for 0.1% of all malignancies. The tumor infiltrates into the deeps in the villous and finger shape. For this reason, it is quite difficult to get surgical margins in the tumor excision and the recurrence is a problem encountered frequently. An excision or Mohs technique of micrographic surgery is suggested by leaving a surgical space up to 5 cm from the tumor margines. In this case report, a case with DFSP atypically subcutaneous localized on superficial parotis gland was presented. It should be kept in mind that probability of the microscopic spread is high in these patients and they should be followed by reminding that the disease can recur in the following long years.

Keywords

Subcutaneous, dermatofibrosarcoma protuberans (DFSP), parotid gland, and superficial parotidectomy

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