A great mimicker of mastoiditis: Multisystem Langerhans’ cell histiocytosis

Year 2020, Volume: 10 Issue: 1, 296 - 299, 25.04.2020

Foong Seong Kın , Ong Cheng Aı , Faezahtul Arbaeyah Hussaın , Bee See Goh

https://doi.org/10.32448/entupdates.673014

Abstract

Langerhans’ cell histiocytosis (LCH) is a rare group of diseases characterized by abnormal clonal proliferation of Langerhans cells in one or more systems. LCH can occur in any system. We report a case of bilateral otologic LCH that presented as a case of mastoiditis. Despite multiple courses of antibiotics, there was no improvement. Subsequent excision biopsy of a postauricular mass confirmed the diagnosis of LCH. The patient responded well to chemotherapy.

Keywords

Histiocytosis, Langerhans-Cell, otological diseases, mastoiditis

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