Abstract
Kesintili arkus aorta nadir rastlanan, fatal seyirli konjenital kardiyak bir anomali olup, aorta ascendens ile aorta descendens arasındaki bir segmentte atrezinin olması şeklinde tanımlanır ve %98 oranında diğer kardiovasküler anomalilerle birlikte bulunur. Üç tipi mevcuttur. Tip A’ da kesinti, a. subclavia sinistra’nın distalindedir. Tip B’de, a. carotis communis sinistra ile a. subclavia sinistra, tip C’de, a. carotis communis sinistra ile a. carotis communis dextra arasındadır. Selçuk Üniversitesi pediatrik kardiyoloji kliniğine başvuran postnatal 5. gününde bir erkek bebeğin çekilen ekokardiyografisinde; truncus brachiocephalicus’un distalinden itibaren tip B kesintili arkus aorta, ventriküler septal defekt, biküspit aorta, patent ductus arteriosus, atrial septal defekt, annulus aorticus hipoplazisi tespit edildi. Bilgisayarlı tomografi anjiyografisinde ise, a. carotis communis sinistra ile a. subclavia sinistra arasında bağlantı olmadığı görüldü. Bu vakada, arcus aorta anomalisi ve eşlik eden diğer kardiovasküler anomalilerin erken tanı ve tedavisinde radyolojik görüntüleme yöntemlerinin önemi vurgulanmaktadır
References
- Arıncı K, Elhan A, 2016. Anatomi, Güneş Tıp Kitabevleri Ankara, 2016; 21-2.
- Arifoğlu Y. Her Yönüyle Anatomi, İstanbul Tıp Kitabevi İs- tanbul, 2016; 254-5.
- Goo HW, Park IS, Ko JK, et al. Radiographics. 2003 ;23 Spec NO: S147-65.
- Park MK 1996 Specific congenital heart defects, obstructive lesions. Pediatric cardiology for practitioners. Mosby Year Book, St. Louis, pp 173-5.
- Yang DH, Goo HW, Seo DM, et al. Multislice CT anjiog- raphy of interrupted aortic arch. Pediatr Radiol 2008; 38: 89-100.
- Van Praagh R, Bernhard W, Rosenthal A, et al:Interrupted aortic arch: surgical treatment. Am J Cardiol 27:200, 1971.
- Schreiber C, Mazzitelli D, Haehnel JC, Lorenz HP, Meis- ner H. The interrupted aortic arch: an overwiew after 20 years of surgical treatment. Eur J Cardiothorac Surg 1997; 12:466-9.
- Wong CK, Cheng CH, Lau CP, Leung WH, Chan FL. Inter- rupted aortic arch in an asymptomatic adult.Cheat 1989;98: 678-9.
- Rangel A, Chavez E, Espinosa I. Interruption of the aortic arch in adults. Arch Inst Cardiol Max 199:89: 144-8.
- Ruckman RN. Anomalies of the aortic arch complex. In Adams FH, Emmanoilides GC, Riemenschneider TA. He- art Disease in Infants, Children and Adolescent. Baltimore, Williams and wilkins, 1989; 256.
- Akçevin A. Arkus aorta anomalileri. Bozer AY. Kalp Hasta- lıkları ve Cerrahisi, Ankara, Ayyıldız Matbaası, 1985; 186.
- Dillman ve Cohen RA, Frush DP, Donnely LF. Data acquisi- tion for pediatric CT anjiography: Problems and solutions. Pediatr Radiol 2000; 30:813-22.
- Dische MR, Tsai M, Baltove HA: Solitary interruption of the arc of aorta. Am J Cardiol 35:271, 1975.
- Baspinar O, Baysal T, Oran B, Karaaslan S. Kesintili arkus aorta sendromu. S.Ü. Tıp Fak. Derg, 2003; 19: 53-5.
- Cinar A, Haliloglu M, Karagoz T, ve ark. Pediatr Radiol. 2004:901-3.
- Katz M,Rozenman J, Szienberg A,Itzchak Y. Spiral CT and 3D image reconstruction of vaskuler rings and associated tracheobronchial anomalies. J Comput Assist tomogr 1995; 19: 564-8.
- Goudar SP, Shah SS, Shirali GS. Echocardiography of coar- ctation of the aorta, aortic arch hypoplasia and arch inter- ruption: strategies for evaluation of the aortic arch. Cardiol Young 2016 ; 26: 1553-62.
Abstract
Interrupted aortic arch is a rare, fatal, congenital cardiac anomaly characterized by the presence of a segmental atresia between the descending and ascending aorta. In type A, the interruption is distal to left subclavian artery. In type B, between left common carotid artery and left subclavian artery; in type C, between left and right common carotid artery. Interrupted aortic arch is present to 98% with other cardiovascular anomalies. Echocardiography of a male baby at the 5th postnatal day referring to Selçuk University pediatric cardiology clinic revealed; type B interrupted aortic arch starting from distal truncus brachiocephalicus, ventricular septal defect, bicuspid aorta, patent ductus arteriosus, atrial septal defect and aortic annulus hipoplasia. The computer tomograpy angiography revealed interruption between left common carotid artery and left subclavian artery. This study highlights the importance of radiologic imaging methods in the early diagnosis and treatment of aortic arch anomaly and accompanying other cardiovascular anomalies
References
- Arıncı K, Elhan A, 2016. Anatomi, Güneş Tıp Kitabevleri Ankara, 2016; 21-2.
- Arifoğlu Y. Her Yönüyle Anatomi, İstanbul Tıp Kitabevi İs- tanbul, 2016; 254-5.
- Goo HW, Park IS, Ko JK, et al. Radiographics. 2003 ;23 Spec NO: S147-65.
- Park MK 1996 Specific congenital heart defects, obstructive lesions. Pediatric cardiology for practitioners. Mosby Year Book, St. Louis, pp 173-5.
- Yang DH, Goo HW, Seo DM, et al. Multislice CT anjiog- raphy of interrupted aortic arch. Pediatr Radiol 2008; 38: 89-100.
- Van Praagh R, Bernhard W, Rosenthal A, et al:Interrupted aortic arch: surgical treatment. Am J Cardiol 27:200, 1971.
- Schreiber C, Mazzitelli D, Haehnel JC, Lorenz HP, Meis- ner H. The interrupted aortic arch: an overwiew after 20 years of surgical treatment. Eur J Cardiothorac Surg 1997; 12:466-9.
- Wong CK, Cheng CH, Lau CP, Leung WH, Chan FL. Inter- rupted aortic arch in an asymptomatic adult.Cheat 1989;98: 678-9.
- Rangel A, Chavez E, Espinosa I. Interruption of the aortic arch in adults. Arch Inst Cardiol Max 199:89: 144-8.
- Ruckman RN. Anomalies of the aortic arch complex. In Adams FH, Emmanoilides GC, Riemenschneider TA. He- art Disease in Infants, Children and Adolescent. Baltimore, Williams and wilkins, 1989; 256.
- Akçevin A. Arkus aorta anomalileri. Bozer AY. Kalp Hasta- lıkları ve Cerrahisi, Ankara, Ayyıldız Matbaası, 1985; 186.
- Dillman ve Cohen RA, Frush DP, Donnely LF. Data acquisi- tion for pediatric CT anjiography: Problems and solutions. Pediatr Radiol 2000; 30:813-22.
- Dische MR, Tsai M, Baltove HA: Solitary interruption of the arc of aorta. Am J Cardiol 35:271, 1975.
- Baspinar O, Baysal T, Oran B, Karaaslan S. Kesintili arkus aorta sendromu. S.Ü. Tıp Fak. Derg, 2003; 19: 53-5.
- Cinar A, Haliloglu M, Karagoz T, ve ark. Pediatr Radiol. 2004:901-3.
- Katz M,Rozenman J, Szienberg A,Itzchak Y. Spiral CT and 3D image reconstruction of vaskuler rings and associated tracheobronchial anomalies. J Comput Assist tomogr 1995; 19: 564-8.
- Goudar SP, Shah SS, Shirali GS. Echocardiography of coar- ctation of the aorta, aortic arch hypoplasia and arch inter- ruption: strategies for evaluation of the aortic arch. Cardiol Young 2016 ; 26: 1553-62.
Details
| Primary Language | Turkish |
|---|---|
| Journal Section | Case Report |
| Authors | |
| Publication Date | January 1, 2019 |
| Published in Issue | Year 2019 Volume: 29 Issue: 1 |
Journal of General Medicine is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License (CC BY NC).