A case of primary pancreatic lymphoma followed in remision in the 9th year

Abstract

Primary pancreatic lymphoma (PPL) is a rare form of ekstranodal, lymphomas, comprising 0.2-4.9% of pancreatic masses and <1% of all malignant lymphomas. Due to the rarity of PPL and nonspecific clinical symptoms and imaging, differentiation of PPL from adenocarcinoma is difficult without histopathologic diagnosis. Many patients with primary pancreatic lymphoma are diagnosed after radical surgery due to difficulties in diagnosis. Many patients with primary pancreatic lymphoma can be diagnosed after radical surgical treatments due to diagnostic difficulties. A 70-year-old patient presenting with abdominal pain was detected to have pancreatic mass. The post-operative pathologic outcome was reported as T-rich B-cell lymphoma. The patient was followed with complete remission after receiving six cycles of chemotherapy. This case report emphasizes the importance of distinguishing between pancreatic lymphoma and adenocarcinoma because of the different treatment strategies and prognoses.

Keywords

• Lymphoma,Pancreas,Mass

Dokuzuncu yılında remisyonda izlenen primer pankreatik lenfoma tanılı bir olgu

Abstract

Primer pankreatik lenfoma ekstranodal lenfomaların nadir bir formudur. Tüm pankreatik neoplazmların %0.2-4.9’unu,tüm malign lenfomaların ise %1’den azını oluşturur. Pankreatik lenfomaların nadir olarak görülmesi, spesifik olmayan klinik semptomları ve görüntüleme bulgularının özgüllüğünün az olması nedeniyle histolojik tanı olmaksızın pankreatik adenokarsinomadan ayrımı zordur. Tanısal açıdan yaşanan zorluklar nedeniyle primer pankreatik lenfomalı bir çok hastanın tanıları radikal cerrahi tedaviler sonrasında yapılabilmektedir. Epigastrik ağrı şikayeti ile polikliniğimize başvuran 70 yaşında kadın bir hastada pankreas başında kitle tespit edildi. Opere edilen hastanın postoperatif patoloji sonucu diffüz büyük B hücreli lenfoma olarak raporlandı. Hastaya kemoterapi verildi ve tam remisyon elde edildi.Bu vaka sunumu, tedavi stratejileri ve prognozları farklı olduğu için pankreatik lenfoma ve adenokarsinomun ayrımının önemini vurgular.

Keywords

• Lenfoma,Pankreas,Kitle

References

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