Serebral Kalsifikasyon; Fahr Sendromu: Olgu Sunumu

Abstract

Fahr sendromu; bazal ganglionlar, serebellar dentat nukleus ve sentrum semiovalede kalsifikasyon görülmesi ile karakterize bir durumdur. Klinik bulgular sıklıkla parkinsonizm, distoni, tremor, kore, ataksiye ek olarak demans ve duygu durum bozukluklarıdır. Biz de kasılma şikayeti ile başvuran Fahr sendromu saptadığımız bir olguyu klinik, laboratuar ve görüntüleme bulguları ile sunmayı amaçladık. Kasılma şikayeti ile başvuran 74 yaşında erkek hastanın muayenesi normal olarak değerlendirildi. Bilgisayarlı beyin tomografi (BBT) incelemesinde her iki serebellar hemisfer ve bazal ganglionlar hizasında yaygın simetrik kalsifikasyon tespit edildi. Bazal ganglionlar, serebellum ve derin kortikal yapılarda kraniyal BT ile saptanan kalsifikasyonların herhangi bir nedene bağlanamadığı durumlarda Fahr sendromu ayırıcı tanıda düşünülmelidir. 

Keywords

• Bilgisayarlı beyin tomografisi,Fahr sendromu,Serebral kalsifikasyon

Cerebral Calcification; Fahr's Syndrome: A Case Report

Abstract

Fahr 's syndrome is a condition which characterized by the calcification in basal ganglia, cerebellar dentate nucleus and centrum semiovale. Clinical findings are often parkinsonism , dystonia, tremor, chorea ,ataxia in addition to mood disorders and dementia. We aimed to report a case of Fahr's syndrome which is presenting with complaint of contraction clinical, laboratory and imaging findings. Admitted with complaint of contraction 74 -year-old male patient's physical examination was normal. Computed tomography imaging was detected bilaterally symmetrical calcification in both cerebellar hemispheres and basal ganglia. Fahr's syndrome should be considered in the differential diagnosis of unable to connect to any reason detected calcifications in the cranial CTin basal ganglia, cerebellum and deep cortical structures.

Keywords

• Computed brain tomography,Fahr's syndrome,Cerebral calcification

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