Osteogenezis imperfektada anestezi yaklaşımı: olgu sunumu Türkçe

Abstract

Osteogenezis imperfekta osteoporoza sebep olan en sık bağ dokusu hastalığı olup fetal kollajenin matür kollajene dönüşümün bozukluğuyla karakterize genetik bir hastalıktır. Anatomik deformiteler ve trombosit disfonksiyonu anestezi tekniği seçimini etkilemektedir. Havayolu ile ilişkili problemlerin yanında malign hipertermiyi tetikleyebilecek süksinil kolin, inhalasyon ajanları ve antikolinerjik ajanlardan sakınılması gerekmektedir. Bu sunumda femur kırığı nedeniyle operasyon planlanan osteogenezis imperfektalı hastada anestezik yaklaşımın değerlendirilmesi amaçlandı

Keywords

• Osteogenezis imperfekta,larengiyal maskeler,propofol,remifentanil

Anesthetic management of osteogenesis imperfecta: a case report

Abstract

Osteogenesis imperfecta is the most common connective tissue disorder that causes osteoporosis and it is characterized by distransformation of fetal collagen to mature collagen. Anatomic deformities and platelet dysfunction influence the choice of anesthetic technique. Besides the attention to the airway related problems, succinylcholine, inhalation agents, and anticholinergic agents that could trigger malignant hyperthermia should be avoided. In this case report, it was aimed to discuss the anesthetic management in an osteogenesis imperfecta patient who had operated for femur fracture

Keywords

• Osteogenesis imperfecta,laryngeal masks,propofol,remifentanil

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