Serebral Kalsifikasyon; Fahr Sendromu: Olgu Sunumu

Year 2016, Volume: 13 Issue: 2, 180 - 183, 29.08.2016

Cebrail Öztürk Selim Bozkurt , Vesile Daraoğlu Fatih Nazmi Yaman , Mehmet Kubilay Gökçe

Abstract

Fahr sendromu; bazal ganglionlar, serebellar dentat nukleus ve sentrum semiovalede kalsifikasyon
görülmesi ile karakterize bir durumdur. Klinik bulgular sıklıkla parkinsonizm, distoni, tremor, kore,
ataksiye ek olarak demans ve duygu durum bozukluklarıdır. Biz de kasılma şikayeti ile başvuran Fahr
sendromu saptadığımız bir olguyu klinik, laboratuar ve görüntüleme bulguları ile sunmayı amaçladık.
Kasılma şikayeti ile başvuran 74 yaşında erkek hastanın muayenesi normal olarak değerlendirildi.
Bilgisayarlı beyin tomografi (BBT) incelemesinde her iki serebellar hemisfer ve bazal ganglionlar hizasında
yaygın simetrik kalsifikasyon tespit edildi. Bazal ganglionlar, serebellum ve derin kortikal yapılarda
kraniyal BT ile saptanan kalsifikasyonların herhangi bir nedene bağlanamadığı durumlarda Fahr sendromu
ayırıcı tanıda düşünülmelidir. 

Keywords

Bilgisayarlı beyin tomografisi, Fahr sendromu, Serebral kalsifikasyon

Cerebral Calcification; Fahr's Syndrome: A Case Report

Abstract

Fahr 's syndrome is a condition which characterized by the calcification in basal ganglia, cerebellar dentate
nucleus and centrum semiovale. Clinical findings are often parkinsonism , dystonia, tremor, chorea ,ataxia
in addition to mood disorders and dementia. We aimed to report a case of Fahr's syndrome which is
presenting with complaint of contraction clinical, laboratory and imaging findings. Admitted with complaint
of contraction 74 -year-old male patient's physical examination was normal. Computed tomography
imaging was detected bilaterally symmetrical calcification in both cerebellar hemispheres and basal
ganglia. Fahr's syndrome should be considered in the differential diagnosis of unable to connect to any
reason detected calcifications in the cranial CTin basal ganglia, cerebellum and deep cortical structures.

Keywords

Computed brain tomography, Fahr's syndrome, Cerebral calcification

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