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Ebstein Anomalisine Eşlik Eden Atriyal Septal Defekt

Year 2006, Volume: 3 Issue: 3, 89 - 91, 01.12.2006

Abstract

Ebstein anomalisi 1866 yılında Wilhelm Ebstein tarafından tanımlanmıştır. Ebstein anomalisi tüm konjenital kalp anomalilerinin % 1 ini oluşturmaktadır. Sıklıkla Pulmoner stenoz veya atrezi, Atriyal Septal Defekt, Ventriküler Septal Defekt ve Fallot Tetrolojisi eşlik eder. Hastalarda genel olarak 3 temel patofizyolojik durum vardır. Sağ ventrikül anomalileri,trikuspit kapak anomalileri,aksesuar ileti yolları WPW sendromu . Medikal tedavisinde konjestif kalp yetmezliği, aritmiler ve bakteriyel endokardit proflaksisi yapılmaktadır. Cerrahi tedavide ise mekanik veya bioprotez kapak replasmanı, kapağın plastik rekonstriksiyonu veya replasman ile rekonstriksiyon yapılabilir.Ebstein anomalisi nadir konjenital kalp hastalıklarından biri olması nedeniyle, kliniğimizde tedavi olan bir olgu literatür bilgileri verilerek sunulmaktadır

References

  • 1-Attenhofer Jost CH, Connolly HM, Edwards WD, Hayes D, Warnes CA, Danielson GK Ebstein's anomaly – review of a multifaceted congenital cardiac condition. Circulation.2007;115:277- 285.
  • 2-Giles JJ.Bannigan JG Teratogenic and developmental effects of lithium. Curr Pharm Des 2006;12(12):1531- 41.
  • 3-Kirklin/Barratt-Boyes Cardiac Surgery .Third Edition 2003 vol .2 -1177
  • 4-Renfu Z, Zengwei W, Hongyu Z, Handong G, Nanbin Z, Xinmin L, et al. Experience in corrective surgery for Ebstein's anomaly in 139 patients Cardiovascular Surgery Institute, Shenyang Northern Hospital, Shenyang Liaoning, Peoples' Republic of China J Heart Valve Dis.2001 May;10(3):396-8.
  • 5-Nagdyman N, Ewert P, Stiller B, Riesenkampff E, Fleck T, Lange PE, Hetzer R. -Ebstein's anomaly: long-term results after modified reconstruction of tricuspid valve without ventricle plication Z Kardiol. 2003 Sep;92 (9): 730- 4.
  • 6-Chauvaud S. Ebstein's malformation. surgical treatment and - results. Thorac Cardiovasc Surg. 2000 Aug;48(4):220- 3.
  • 7-Sarris GE, Giannopoulos NM, Tsoutsinos AJ, Chatzis AK, Kirvassilis G, Berggren H et al. Heart Results of surgery for Ebstein anomaly: a multicenter study from the European Congenital Surgeons Association Onassis Cardiac Surgery Center, Athens, Greece. J Thorac Cardiovasc Surg. 2006 Jul;132(1):50 -57.
  • 8- Chauvaud S, Berrebi A, d'Attellis N, Mousseaux E, Hernigou A, Carpentier A. Ebstein's anomaly: repair based on functional analysis. Eur J Cardiothorac Surg 2003; 23:525- 531.
  • 9-Rizzoli G, Guglielmi, Toscana G, Pistoria V, Venderamin I, Bottio T, et al. Reoperations for acute prosthetic thrombosis and pannus: an assessment of rates, relationship and risk. Eur J Cardiothorac Surg. 1999 Jul;16(1): 74-80.

Atrıal Septal Defect Wıth Ebsteın’s Anomaly

Year 2006, Volume: 3 Issue: 3, 89 - 91, 01.12.2006

Abstract

Ebstein anomally described by Willhelm Ebstein in 1866. Ebstein anomaly accounting for 1/100 of all cases of congenital heart disease. Pulmoner stenosis or atresia is most common accompaying defect. Others include ASD,VSD,TOF,PDA.Three primary pathophisiologic features predominant patients with anomaly. Right ventricle abnormalities, tricuspidal valve abnormalities, accessory conduction pathways WPW syndrome . Medical treatment will consist of the treatment of the congestive heart failure, arrhytmias and prevention of bacterial endocarditis. Mechanical or bioprothesis valve replacement or valve plastic reconstruction, or reconstruction with replacement have been used in surgical treatments. We report one case of this rare Ebstein’s anomaly with the review of the literature

References

  • 1-Attenhofer Jost CH, Connolly HM, Edwards WD, Hayes D, Warnes CA, Danielson GK Ebstein's anomaly – review of a multifaceted congenital cardiac condition. Circulation.2007;115:277- 285.
  • 2-Giles JJ.Bannigan JG Teratogenic and developmental effects of lithium. Curr Pharm Des 2006;12(12):1531- 41.
  • 3-Kirklin/Barratt-Boyes Cardiac Surgery .Third Edition 2003 vol .2 -1177
  • 4-Renfu Z, Zengwei W, Hongyu Z, Handong G, Nanbin Z, Xinmin L, et al. Experience in corrective surgery for Ebstein's anomaly in 139 patients Cardiovascular Surgery Institute, Shenyang Northern Hospital, Shenyang Liaoning, Peoples' Republic of China J Heart Valve Dis.2001 May;10(3):396-8.
  • 5-Nagdyman N, Ewert P, Stiller B, Riesenkampff E, Fleck T, Lange PE, Hetzer R. -Ebstein's anomaly: long-term results after modified reconstruction of tricuspid valve without ventricle plication Z Kardiol. 2003 Sep;92 (9): 730- 4.
  • 6-Chauvaud S. Ebstein's malformation. surgical treatment and - results. Thorac Cardiovasc Surg. 2000 Aug;48(4):220- 3.
  • 7-Sarris GE, Giannopoulos NM, Tsoutsinos AJ, Chatzis AK, Kirvassilis G, Berggren H et al. Heart Results of surgery for Ebstein anomaly: a multicenter study from the European Congenital Surgeons Association Onassis Cardiac Surgery Center, Athens, Greece. J Thorac Cardiovasc Surg. 2006 Jul;132(1):50 -57.
  • 8- Chauvaud S, Berrebi A, d'Attellis N, Mousseaux E, Hernigou A, Carpentier A. Ebstein's anomaly: repair based on functional analysis. Eur J Cardiothorac Surg 2003; 23:525- 531.
  • 9-Rizzoli G, Guglielmi, Toscana G, Pistoria V, Venderamin I, Bottio T, et al. Reoperations for acute prosthetic thrombosis and pannus: an assessment of rates, relationship and risk. Eur J Cardiothorac Surg. 1999 Jul;16(1): 74-80.
There are 9 citations in total.

Details

Primary Language Turkish
Journal Section Research Article
Authors

Deniz Demir This is me

Mehmet Salih Aydın This is me

Cüneyt Şelli This is me

Aydemir Koçarslan This is me

Mehmet Halit Andaç This is me

Publication Date December 1, 2006
Published in Issue Year 2006 Volume: 3 Issue: 3

Cite

Vancouver Demir D, Aydın MS, Şelli C, Koçarslan A, Andaç MH. Ebstein Anomalisine Eşlik Eden Atriyal Septal Defekt. Harran Üniversitesi Tıp Fakültesi Dergisi. 2006;3(3):89-91.

Harran Üniversitesi Tıp Fakültesi Dergisi  / Journal of Harran University Medical Faculty