OLGU SUNUMU: PARATESTİKÜLER RABDOMİYOSARKOM

Öz

Paratestiküler Rabdomiyosarkom İntraskrotal bölgede görülen tümörler, testis ve paratestiküler yapılardan kaynaklanabilmektedirler. Paratestiküler tümörler nadir olarak görülmektedirler 1 . Malign paratestiküler tümörlerin %46,4’ünü liposarkom, %20’sini leiomyosarkom, %13’ünü malign fibröz histiositom ve %9’unu embryonel rabdomiyosarkom oluşturmaktadır 2 . RMS Rabdomiyosarkom sıklıkla çocuk ve adolesan yaş grubunda görülür ve hastalar ağrısız skrotal kitle ile başvurur 3 . Bu çalışmada sol radikal orşiektomi sonrası saptanan ve nadir görülen paratestiküler embriyonel rabdomiyosarkom olgusu literatür eşliğinde sunulmuştur

Anahtar Kelimeler

• Rabdomiyosarkom,testis kanseri,paratestiküler kitle

CASE REPORT: PARATESTICULAR RHABDOMYOSARCOMA

Abstract

Paratesticular Rhabdomyosarcoma Intrascrotal tumors may originate from testicular or paratesticular tissue. Tumors in the paratesticular region are seen rarely 1 . Among the malignant tumors, the most common histotype is liposarcoma 46.4% , followed by leiomyosarcoma LMS 20% , malignant fibrous histiocytomas MFH 13% , and embryonal rhabdomyosarcoma 9% 2 . Rhabdomyosarcoma is frequently seen in children and adolescents. The most common symptom is painless swelling in scrotum 3 . In this paper we present a case who was diagnosed as paratesticular embryonal rhabdomyosarcoma in histological examination of radical orchiectomy material

Keywords

• Rhabdomyosarcoma,testicular cancer,paratesticular mass

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