Double Aortic Arch And Ventricular Septal Defect With Pulmonary Atresia: A Rare Combination In A Congenital Heart Surgery

Abstract

Rare combinations of congenital heart pathologies can make the management of the surgical repair difficult and may complicate the procedure. We would introduce a newborn diagnosed with ventricular septal defect, pulmonary atresia and double aortic arch and the successful palliative surgery with shunt procedure of the patient. Atypical ductus, double aortic arch and the different configuration of its branches can complicate the usual shunt procedure. Variations in vascular structures may be the reason for complications in congenital heart surgery. Before planning the surgical procedure, vascular anatomy should be presented in detail even for palliative operations. Blalock-Taussig shunt can be performed safely in the case of a double aortic arch.

Keywords

• Double aortic arch
• ventricular septal defect
• pulmonary atresia

References

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