Double Aortic Arch And Ventricular Septal Defect With Pulmonary Atresia: A Rare Combination In A Congenital Heart Surgery

Öz

Rare combinations of congenital heart pathologies can make the management of the surgical repair difficult and may complicate the procedure. We would introduce a newborn diagnosed with ventricular septal defect, pulmonary atresia and double aortic arch and the successful palliative surgery with shunt procedure of the patient. Atypical ductus, double aortic arch and the different configuration of its branches can complicate the usual shunt procedure. Variations in vascular structures may be the reason for complications in congenital heart surgery. Before planning the surgical procedure, vascular anatomy should be presented in detail even for palliative operations. Blalock-Taussig shunt can be performed safely in the case of a double aortic arch.

Anahtar Kelimeler

• Double aortic arch
• ventricular septal defect
• pulmonary atresia

Kaynakça

1. Dixon CM, Dyar D, Aurigemma D, Printz B F, Hegde S, Ryan J et al. Double choker: Double aortic arch with bilateral aortic coarctation associated with heterotaxy-asplenia syndrome and complex atrioventricular canal defect. CASE (Phila) Cardiovasc Imaging Case Reports 2020; 4(3): 142–5. google scholar
2. Priya S, Thomas R, Nagpal P, Sharma A, Steigner M. Congenital anomalies of the aortic arch. Cardiovasc Diagn Ther 2018(Suppl 1); 8: S26–S44. google scholar
3. Tiraboschi R, Manasse E, Parenzan L. Case report tetralogy of Fallot associated with a double aortic arch palliation with a prosthetic tube graft. Tex Heart Inst J 1988; 15(2): 131-3. google scholar
4. Thankavel PP, Brown PS, Lemler MS. Left-dominant double aortic arch in critical pulmonary stenosis and ventricular septal defect. Pediatr Cardiol 2012; 33(8): 1469–71. google scholar
5. Atik E. Clinicoradiological Session Case 6/2012-Newborn with pulmonary atresia, ventricular septal defect and double aortic arch complementary examinations. Arq Bras Cardiol 2012; 99(3): e128-e130. google scholar