Congenital Cystic Adenomatoid Malformation As A Rare Cause Of Respiratory Distress In Newborn

Abstract

Congenital cystic adenomatoid malformation CCAM is a rare lung disorder developed as a result of the improper fusion of the bronchial buds with the alveolar mesenchyme during embryological development. Depending on the type of lesion, CCAM tissue pressure in newborns may cause respiratory distress and may later manifest itself as recurrent pulmonary infections in young adults. Lobectomy has been recommended in symptomatic. patients; whereas surgical intervention may be delayed in asymptomatic patients for 6-12 months.

Keywords

• Congenital Cystic Adenomatoid Malformation,Newborn,Lung,Lobectomy,Respiratory Distress

Yenidoğanda Nadir Bir Solunum Sıkıntısı Nedeni: Konjenital Kistik Adenoid Malformasyon

Abstract

Konjenital kistik adenoid malformasyon KKAM bronşiyal tomurcukların alveolar mezenşimle uygun şekilde birleşememesi sonucu ortaya çıkan akciğerin nadir görülen embryolojik gelişim bozukluğudur. Lezyonun tipine göre, KKAM fonksiyon gören pulmoner dokuya bası ile yenidoğanlarda solunum güçlüğüne yol açabilir veya genç erişkinde rekürren akciğer enfeksiyonu ile kendini gösterebilir. Semptomatik olgularda lobektemi önerilmekte, asemptomatik olgularda ise 6-12 aya kadar girişimin geciktirilebileceği bildirilmektedir.

Keywords

• Konjenital Kistik Adenomatoid Malformasyon,Yenidoğan,Akciğer,Lobektomi,Respiratuvar Distress

References

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