Rare Presentation of Schmahmann’s Syndrome in Dandy-Walkers Malformation - A Case Report

Abstract

The aim of this case report is to highlight the varied presentation of neurological disorders and the need for detailed evalution of the acute manisfestations of psychiatric symptoms. We report the case of a 17 year old boy presenting with complaints of acute onset of behavioural symptoms. We have briefly reviewed and discussed the clinical , diagnostic aspects of schmahmanns syndrome and therapeutic aspects of behavioural symptoms in dandy walkers malformation.

Keywords

• Dandy Walker Malformation
• Schmahmann’s Syndrome
• Disinhibition
• Repetition
• CCAS scale.

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