ANTİFOSFOLİPİT ANTİKOR SENDROMLU HASTADA TRİKÜSPİT KAPAKTA PAPİLLER FİBROELASTOM VE NONBAKTERİYEL TROMBOTİK ENDOKARDİT BİRLİKTELİĞİ OLGU SUNUMU

Abstract

Primer kardiyak tümörler nadir görülmekte olup, genellikle benign karakterlidir. Bu tümörler arasında en sık rastlananlardan biri papiller fibroelastomdur . Papiller fibroelastom genellikle asemptomatik seyretse de, ciddi embolik komplikasyonlara yol açabilir. Bu olgu sunumunda, 42 yaşında erkek antifosfolipid antikor sendromu tanısı bulunan ve triküspit kapakta papiller fibroelastom zemininde gelişen nonbakteriyel trombotik endokardit vakası sunulmuştur Patolojik inceleme, papiller fibroelastom ve nonbakteriyel trombotik endokardit lehine değerlendirilmiştir. Olgu, papiller fibroelastom ve nonbakteriyel trombotik endokardit birlikteliğinin antifosfolipid antikor sendromu ile ilişkili olabileceğini göstermesi açısından dikkat çekicidir. Ayrıca, romatolojik hastalıkların kardiyak tutulumu ve kapak patolojilerinin embolik riskleri açısından dikkatli olunması gerektiği vurgulanmaktadır.

Keywords

• Papiller fibroelastom
• nonbakteriyel trombotik endokardit
• antifosfolipid antikor sendromu
• triküspit kapak replasmanı
• kardiyak tümör

Case Report: Concomitant Papillary Fibroelastoma and Non-Bacterial Thrombotic Endocarditis of the Tricuspid Valve in a Patient with Antiphospholipid Antibody Syndrome

Abstract

Primary cardiac tumors are rare and usually benign. Among these, papillary fibroelastoma is one of the most frequently encountered types. Although often asymptomatic, papillary fibroelastoma can lead some serious embolic complications. This case report presents a 42-year-old male patient diagnosed with antiphospholipid antibody syndrome, who developed nonbacterial thrombotic endocarditis on a tricuspid valve papillary fibroelastoma. Histopathological findings supported a diagnosis of papillary fibroelastoma with coexisting nonbacterial thrombotic endocarditis, This case highlights the association between papillary fibroelastoma and nonbacterial thrombotic endocarditis in the context of antiphospholipid antibody syndrome, emphasizing the importance of clinical vigilance regarding cardiac involvement in rheumatologic diseases and the embolic potential of valvular masses.

Keywords

• Papillary fibroelastoma
• nonbacterial thrombotic endocarditis
• antiphospholipid antibody syndrome
• tricuspid valve replacement
• cardiac tumor

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