Urrets-Zavalia Syndrome After Penetrating Keratoplasty

Abstract

Urrets-Zavalia syndrome (UZS) was first described in 1963 as a case of atrophic dilated pupil accompanied by secondary glaucoma, which developed after penetrating keratoplasty (PKP) using mydriatics in patients with keratoconus. Urrets-Zavalia syndrome is a surgical complication in which the pupil remains fixed and dilated after an intraocular surgical intervention. Although it is thought to be especially related to penetrating keratoplasty, it can also be seen after other intraocular surgical procedures (Trabeculectomy, deep anterior lamellar keratoplasty, cataract, goniotomy). The most important risk factor is iris ischemia due to increased intraocular pressure during or after surgery. The study aimed to present the management of Urrets-Zavalia Syndrome, which developed after penetrating keratoplasty in two patients with left eye corneal granular dystrophy and left eye keratoconus.

Keywords

• penetrating keratoplasty
• Urrest-Zavalia syndrome
• keratoconus
• corneal dystrophy

References

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