Birinci Basamak Hekimleri için Zor Bir Tanı: PFAPA Sendromu (Periyodik Ateş, Aftöz Stomatit, Farenjit ve Adenit birlikteliği)

Abstract

PFAPA, periyodik yüksek ateş epizotları, aftöz stomatit, farenjit ve servikal adenit ile karakterize, kalıtsal olmayan bir sendromdur. Özellikle stomatit, ateş yüksekliği, farenjit ve adenitten oluşan klinik tabloların aile hekimliği pediatrik hasta popülasyonunda önemli bir yer tuttuğu bilinmektedir. Bu derleme ile amacımız birinci basamak hekimleri tarafından çok iyi bilinmeyen PFAPA sendromu hakkında bilgi vermektir. PFAPA Sendromu çok sık görülmemekle birlikte periyodik ateş yüksekliği, farenjit ve adenit tablosuyla aile hekimine başvuran çocukların ayırıcı tanısında düşünülmelidir

Keywords

• Aile Hekimliği
• Birinci Basamak
• Ateş
• Tonsillit

A Diagnostic Challenge for Primary Care Physicians: PFAPA Syndrome (Periodic Fevers With Aphthous Stomatitis, Pharyngitis, And Adenitis)

Abstract

PFAPA, characterized by periodic episodes of high fever, aphthous stomatitis, pharyngitis and cervical adenitis, is a non-hereditary syndrome. Admission with stomatitis, fever, pharyngitis and adenitis is known to hold an important place in the pediatric patient population of family medicine practice. Our objective with this review is to provide information about PFAPA syndrome, which is not yet well-recognized by primary care physicians. PFAPA is a non-common disorder, but should be kept in mind for the patients that admitted with periodic fever, pharyngitis, and adenitis.

Keywords

• Family Medicine
• Primary Care
• Fever
• Tonsillitis

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