Approach to Chronic Liver Diseases in Children

Abstract

Chronic liver disease (CHD) is a chronic process in the liver parenchyma with progressive destruction and regeneration resulting in fibrosis and cirrhosis. Although many different diseases, ranging from infectious causes to autoimmune causes, are included in the etiology, patients present with similar clinical findings in childhood. A detailed history and careful physical examination give remarkable information for diffrential diagnosis. However, specific tests are needed for a definitive diagnosis. Nevertheless, there is still a group with no etiology.

Because of longer life span of these children compared to adults, More attention should be paid to the complications. Specially nutritional status, bone metabolism and vaccination programs of these patients should be monitored closely. When necessary, patients should be treated earlier.

Keywords

• Chronic liver disease,child,complications

ÇOCUKLARDA KRONİK KARACİĞER HASTALIKLARINA YAKLAŞIM

Abstract

Kronik karaciğer hastalığı (KKH), karaciğer parankiminde progresif bir yıkım ve rejenerasyon ile giden, fibrozis ve siroz ile sonuçlanan kronik bir süreçtir. Enfeksiyöz nedenlerden otoimmun nedenlere kadar birçok farklı hastalık etiyolojisinde rol almasına karşın hastalar karşımıza benzer klinik bulgularla çıkmaktadır. Ayrıntılı bir anamnez ve dikkatli bir fizik muayene ayırıcı tanıda dikkate değer bilgi verir. Ancak kesin tanı için özgül testlere ihtiyaç vardır. Herşeye rağmen etiyolojisi bulunmayan bir grup hala mevcuttur. 

Çocukların önlerinde daha uzun bir yaşam olduğu göz önüne alınarak komplikasyonlar açısından dikkatli olunmalıdır. Özellikle beslenme durumları, kemik metabolizması ve aşı programları yakın takip edilmelidir. Gerekli durumlarda hastalara erken müdahale edilmelidir. 

Keywords

• Kronik karaciğer hastalığı,çocuk,komplikasyonlar

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