Nörofibromatozis Tip 1 Tanılı Gebede Elektif Sezaryen Operasyonunda Spinal Anestezi Yönetimi

Year 2015, Volume: 17 Issue: 2, 46 - 50, 05.01.2016

Gülçin Aydın , Cemile Sayan İsmahan Özbayrak Ferda Yaman İşın Gençay Selim Çolak Ünase Büyükkoçak

https://doi.org/10.24938/kutfd.124922

Abstract

Nörofibromatozis Tip 1 (NF-1) ektodermal ve mezodermal dokulardaki yaygın etkileri nedeniyle otozomal dominant geçiş gösteren kalıtsal bir hastalık grubudur. Periferik sinirlerde multipl nörofibromlar ile karakterize olan hastalıkta kutanöz pigmente lekeler (cafe au lait spots) mevcuttur. Bu nörofibromlar sadece sinir sisteminde değil, orofarinks ve larinkste de bulunarak laringoskopiyi ve endotrakeal entübasyonu zorlaştırabilir. Bu olgu sunumuyla NF-1 tanılı gebe kadında elektif sezaryen operasyonunda spinal anestezi uygulamamızı sunmayı amaçladık.

Keywords

Nörofibromatozis tip 1 , spinal anestezi , sezeryan

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