Primary Extradural Extraosseous Ewing’s Sarcoma of The Thoracic Spinal Canal: A Case Report

Abstract

Ewing’s sarcoma most commonly occurs in bone and only very rarely in the extradural spinal canal. Herein, we present the clinical course, diagnosis, and treatment of a 6-year-old girl admitted with a complaint of strength loss in her right lower extremity. Magnetic resonance imaging revealed an extradural spinal canal tumor extending from level T2 to T5; she underwent laminectomy. The histopathological, immunohistochemical, and molecular cytogenetic data were compatible with Ewing’s sarcoma. We detected no malignant focus on postoperative staging work-up and prescribed postoperative radiotherapy and chemotherapy. A brief review of the literature on primary extradural extraosseous Ewing’s sarcoma of the spinal canal is presented.

Keywords

• extramedullary spinal cord compression,spinal canal,Adjuvant radiotherapy,chemotherapy,Ewing’s sarcoma,spinal canal

Torasik Spinal Kanalın Primer Ekstradural Ekstraosseöz Ewing Sarkomu: Olgu Sunumu

Abstract

Ewing sarkom sıklıkla kemikte gelişir ve ekstradural spinal kanalda oldukça nadirdir. Burada, sağ alt ekstremitede güç kaybı şikâyeti ile başvuran 6 yaşında bir kız çocuğunun klinik seyri, tanı ve tedavisini sunuyoruz. Manyetik rezonans görüntülemesinde T2’den T5’e kadar uzanan ekstradural spinal kanal tümörü mevcuttu. Laminektomi yapıldı. Histopatolojik, immünohistokimyasal ve moleküler sitogenetik incelemeler Ewing sarkom ile uyumluydu. Ameliyat sonrasında yapılan evreleme çalışmalarında herhangi bir malign odak saptanmadı. Postoperatif radyoterapi ve kemoterapi uygulandı. Bu çalışmada, spinal kanalın primer ekstradural ekstraosseöz Ewing sarkom, güncel literatür ışığında kısaca tartışılmıştır.

Keywords

• Ewing sarkom,ekstramedüller spinal kord kompresyonu,kemoterapi,spinal kanal,Adjuvant radyoterapi,spinal kanal

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