Idiopatic Infantile Arterial Calcification: Echocardiography Diagnosis and Successful Treatment

Abstract

Idiopathic infantile arterial calcification is rare disease characterized by medial calcification and intimal proliferation of large and medium size arteries (1).

Prenatal prezantation is usually with nonimmune hidrops and polyhydamnios (2). Although the clinical characteristics in neonatal period is variable, respiratory distress with cardiac failure is the most common finding. Hypertension due to poor compliance caused by diffuse arterial calcification of the vessels is present in most patients.

Clinical experience in treating this rare disorder is limited. We present a neonatal case with Idiopathic infantile arterial calcification who was treated with etidronate disodium, successfully.

Keywords

• Arterial Calcification

References

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