A RARE COMBINATION: BIVENTRICULAR NON-COMPACTION, EBSTEIN’S ANOMALY, WOLF PARKINSON WHITE SYNDROME AND MITRAL VALVE PROLAPSUS

Year 2018, Volume: 1 Issue: 1, 20 - 22, 13.08.2018

Mahmut Uluganyan , Nijad Bakhshaliyev , Asım Enhoş , Nuray Kahraman Ay

Abstract

Ventricular
non-compaction and Ebstein’s anomaly are 2 rare congenital abnormalities. In
some cases both abnormalities share common genetic predisposition. Both
abnormalities could be associated. We report a case of 25-year old male patient
with biventricular non-compaction, Ebstein’s anomaly, mitral valve prolapsus
and Wolf-Parkinson-White syndrome. The combination of these congenital
abnormalities could infer a common genetic predisposition with different
presentation of myocardium and leaflets.

Keywords

Biventricular non-compaction, Ebstein’s Anomaly, Wolf Parkinson White Syndrome, Mitral Valve Prolapsus

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