Zinner Syndrome Versus Herlyn-Werner-Wunderlich syndrome; Rare Congenital Genitourinary Malformations and Literature Review

Year 2024, Volume: 19 Issue: 2, 95 - 102, 29.06.2024

Saim Türkoğlu Cemil Göya Murat Demir

https://doi.org/10.33719/nju1421307

Abstract

Zinner syndrome(ZS) and Herlyn-Werner-Wunderlich syndrome (HWWS) are congenital genitourinary anomalies accompanied by ipsilateral renal agenesis. These syndromes, which can cause symptoms such as infertility, pelvic pain, and bladder irritation, can be diagnosed by digital rectal examination, transrectal and abdominal ultrasonography(US), Computer Tomography(CT) and more ideally Magnetic resonance imaging (MRI). Similar physiopathological processes are observed in both syndromes and urogenital malformations accompany renal agenesis. We aimed to discuss the three cases of ZS in men and two HWWS cases in women, which are rarely observed in the literature.

Keywords

Zinner syndrome, Herlyn-Werner-Wunderlich syndrome, Seminal vesicle cysts, renal agenesis, mullerian duct anomaly, blind hemivagina, uterus didelfis

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