Dental Treatment in Patient with Moebius Syndrome: Case Report

Year 2021, Volume: 12 Issue: 2, 237 - 240, 20.08.2021

Merve Candan , Arife Kaptan

https://doi.org/10.22312/sdusbed.848519

Abstract

The incidence of Moebius syndrome (MS), in which craniofacial anomalies are common, is not fully known and is thought to result from a combination of environmental&genetic factors. Most of the signs and symptoms of MS, are due to the absence or underdevelopment of the 6th and 7th cranial nerves. Craniofacial anomalies are also among the prominent symptoms of MS. Micrognathia, short or unusually shaped tongue and microstomia may seen in MS. Dental treatments of children with MS may need to be done under general anesthesia. However, there are some situations that need to be considered during general anesthesia. The quality of life of individuals affected by this syndrome is negatively affected and they usually need special care. This case report addresses the clinical and dental features of a child with MS and the clinical situations and difficulties encountered during dental treatment. Considering the variable oral symptoms of patients with Moebius syndrome, it is clear that the clinical follow-up of these patients requires a multidisciplinary approach involving dental professionals.

Keywords

Moebius Syndrome, Dental Treatment, Dentistry

Moebius Sendromlu Hastada Dental Tedavi: Olgu Sunumu

Abstract

Kraniyofasiyal anomalilerin sık görüldüğü Moebius sendromunun(MS) insidansı tam olarak bilinmemektedir ve çevresel&genetik faktörlerin kombinasyonundan kaynaklandığı düşünülmektedir. MS’nin belirti ve semptomlarının çoğu, 6. ve 7. kraniyal sinirlerin yokluğundan veya az gelişmesinden kaynaklanır. Kraniyofasiyal anomaliler de MS'nin öne çıkan semptomları arasındadır. MS'de mikrognati, kısa veya alışılmadık şekilli dil ve mikrostomi görülebilir. MS'li çocukların dental tedavilerinin genel anestezi altında yapılması gerekebilir. Ancak genel anestezi sırasında dikkat edilmesi gereken bazı durumlar vardır. Bu sendromdan etkilenen bireylerin yaşam kalitesi olumsuz etkilenir ve genellikle özel bakıma ihtiyaç duyarlar. Bu olgu sunumu, MS’li bir çocuğun klinik ve dental bulgularını, diş tedavisi sırasında karşılaşılan klinik durumları ve zorlukları ele almaktadır. Moebius sendromlu hastaların değişken oral belirtileri göz önüne alındığında, bu hastaların klinik takibinin diş hekimlerinin de yer aldığı multidisipliner bir yaklaşım gerektirdiği açıktır.

Keywords

Moebius Sendromu, Dental Tedavi, Diş Hekimliği

References

• Briegel W, Schimek M, Kamp-Becker I. Moebius sequence and autism spectrum disorders--less frequently associated than formerly thought. Res Dev Disabil. 2010;31(6):1462-6.
• Hatice Mutlu Albayrak, Nuriye Tarakçı, Hüseyin Altunhan, Rahmi Örs, Hüseyin Çaksen. A congenital cranial dysinnervation disorder: Möbius’ syndrome. Turk Pediatri Ars . 2017;52(3):165-8.
• Bartzela TN, Carels C, Maltha JC. Update on 13 Syndromes Affecting Craniofacial and Dental Structures. Front Physiol. 2017; 8: 1038. Doi: 10.3389/fphys.2017.01038
• Ghosh R, Shetty V, Hegde S, Babu GS, Ajila V, Kishore P N, vd. Rare features associated with Mobius syndrome: Report of two cases. J Dent Res Dent Clin Dent Prospects. 2017;11(1):60-5.
• Briegel W, Schimek M, Knapp D, Holderbach R, Wenzel P, Knapp E-M. Cognitive evaluation in children and adolescents with Möbius sequence. Child Care Health Dev. 2009;35(5):650-5.
• Moebius syndrome. Genetics Home Reference. Erişim tarihi: 27 Şubat 2020. Erişim adresi: https://ghr.nlm.nih.gov/condition/moebius-syndrome
• Sjögreen L, Andersson-Norinder J, Jacobsson C. Development of speech, feeding, eating, and facial expression in Möbius sequence. Int J Pediatr Otorhinolaryngol. 2001;60(3):197-204.
• Pinto MVXDS, Magalhães MHCGD, Nunes FD. Moebius syndrome with oral involvement. International Journal of Paediatric Dentistry. 2002;12(6):446-9.
• Martins Mussi MC, Moffa E, Castro T, Lira Ortega A, Freitas G, Braga M, vd. Salivary parameters and oral health in the Moebius syndrome. Spec Care Dentist. 2016;36(5):265-70.
• Castro T, Ortega AOL, Mussi MC, Braga MM, Gallottini M. Caries Experience in Individuals with Moebius Syndrome. Pediatr Dent. 2016;38(1):68-71.
• Gondipalli P, Tobias JD. Anesthetic implications of Möbius syndrome. J Clin Anesth. 2006;18(1):55-9.
• Moebius syndrome. Children’s Craniofacial Association. Erişim tarihi: 27 Şubat 2020. Erişim adresi: https://ccakids.org/moebius-syndrome.html
• Nussbaum BL. Dental care for patients who are unable to open their mouths. Dent Clin North Am. 2009;53(2):323-8, x.