Swyer-James (Macleod) Sendromu (Bir Olgu nedeniyle)

Abstract

44 yaþýnda kadýn hasta öksürük ve efor dispnesi yakýnmasýyla kliniðimize baþvurdu. Akciðer grafisinde sol hemitoraksta hiperlüsensi, akciðerlerin bilgisayarlý tomografisinde (BT) sol akciðerde havalanma artýþý, damarlanmada ise azalma saptandý. Sintigrafide sol akciðerde diffüz, uyumlu ventilasyon/perfüzyon defekti mevcuttu. Pulmoner anjiografide sol ana pulmoner arter ve dallarýnda hipoplazi görüldü. Bu bulgularla hastaya Swyer-James (Macleods) sendromu tanýsý kondu. Bu nadir klinik olguyu literatür eþliðinde sunmak istedik.

Keywords

• Swyer-James Sendromu
• Macleod sendromu
• hiperlüsensi
• anjiografi

Swyer-James (Macleod’s) Syndrome: A case report

Abstract

44 year-old female patient with a history of cough pain and exercise induced dyspnea admitted to our clinic. The chest x-ray revealed hyperlucency of the left lung. Computerized tomography with increased aeration and decreased vascular structures were observed on the left lung. There was a diffuse matched ventilation/perfusion defect on the left lung. MR angiography showed hypoplastic left main pulmonary artery and its branches. The patient was diagnosed as Unilateral hyperlucent lung syndrome-Swyer-James (Macleods) Syndrome. We wanted to present this rare case in the light of the current literature.

Keywords

• Swyer-James Syndrome
• Macleod’s syndrome
• hyperlucency
• angiography

References

1. Shapiro SD, Snider GL, Rennard SI. Chronic bronchitis and emphysema. In: Murrey JF, Nadel JA (eds). Textbook of Respiratory Medicine.Philadelphia: Elsevier Saunders, 2005; 1115-67.
2. Snider CL: Chronic bronchitis and emphysema. In Murray I, Nadcl JA (eds.): Textbook of respiratory medicine. Philadelphia, WB Saunders Co, 1988;1069- 106.
3. Lucaya J, Gartner S, García-Peña P, Cobos N, Roca I, Liñan S. Spectrum of manifestations of Swyer-James- Macleod’s syndrome. J Comput Assist Tomogr 1998; 22(4):592-97.
4. Swyer PR, James GCW. A case of unilateral pulmonary emphysema. Thorax 1953; 8(2):133-6.
5. Macleod WM. Abnormal transradiancy of one lung. Thorax 1954;9(2):147-53.
6. Bonmati LM, Perales FR, Catala F, Mata JM, Calonge E. CT findings in Swyer-James syndrome. Radiology 1989; 172(2):477-80.
7. Hekali P, Halttunen P, Korhola O, Korppi-Tommola T. Chronic unilateral hyperlucent lung. A consecutive series of 40 patients. ROFO Fortschr Geb Rontgenstr Nuklear Med 1982; 136(1): 41-8.
8. Chevrolet JC, Junod AF. Characteristics of respiratory functional involvement in MacLeod’s syndrome (or Swyer-James syndrome). Schweiz Med Wochenschr 1987;117(48):1902-09.

9. Stern EJ, Samples TL. Dynamic ultrafast high resolution CT findings in a case of Swyer-James syndrome. Pediatr Radiol 1992; 22(5):350-52.
10. Kiratli PO, Caglar M, Bozkurt MF. Unilateral absence of pulmonary perfusion in Swyer-James syndrome. Clin Nucl Med 1999; 24(9): 706-7.
11. Arslan N, Ilgan S, Ozkan M, Yuksekol I, Bulakbasi N, Pabuscu Y, et al. Utility of ventilation and perfusion scan in the diagnosis of young military recruits with an incidental finding of hyperlucent lung. Nucl Med Commun 2001; 22(5):525-30.
12. Moore AD, Godwin JD, Dietrich PA, Verschekalen JA, Hcndersonn WJ Jr. Swyer- James syndrome. CT findings in eight patients. AJR 1992; 158(6):1211-15.