Swyer-James (Macleod) Sendromu (Bir Olgu nedeniyle)

Year 2010, Volume: 17 Issue: 2, 27 - 30, 30.06.2010

Ünal Şahin , Önder Öztürk , Necla Songür

Abstract

44 yaþýnda kadýn hasta öksürük ve efor dispnesi yakýnmasýyla kliniðimize baþvurdu. Akciðer grafisinde sol hemitoraksta hiperlüsensi, akciðerlerin bilgisayarlý tomografisinde (BT) sol akciðerde havalanma artýþý, damarlanmada ise azalma saptandý. Sintigrafide sol akciðerde diffüz, uyumlu ventilasyon/perfüzyon defekti mevcuttu. Pulmoner anjiografide sol ana pulmoner arter ve dallarýnda hipoplazi görüldü. Bu bulgularla hastaya Swyer-James (Macleods) sendromu tanýsý kondu. Bu nadir klinik olguyu literatür eþliðinde sunmak istedik.

Keywords

Swyer-James Sendromu, Macleod sendromu, hiperlüsensi, anjiografi

Swyer-James (Macleod’s) Syndrome: A case report

Abstract

44 year-old female patient with a history of cough pain and exercise induced dyspnea admitted to our clinic. The chest x-ray revealed hyperlucency of the left lung. Computerized tomography with increased aeration and decreased vascular structures were observed on the left lung. There was a diffuse matched ventilation/perfusion defect on the left lung. MR angiography showed hypoplastic left main pulmonary artery and its branches. The patient was diagnosed as Unilateral hyperlucent lung syndrome-Swyer-James (Macleods) Syndrome. We wanted to present this rare case in the light of the current literature.

Keywords

Swyer-James Syndrome, Macleod’s syndrome, hyperlucency, angiography

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